Document Detail


Primary distal renal tubular acidosis as a result of a gradient defect.
MedLine Citation:
PMID:  8604714     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
It has been generally accepted that primary distal renal tubular acidosis (DRTA) is the result of a defect in proton secretion in the distal nephron (secretory defect). We report an infant with DRTA, evidenced by spontaneous hyperchloremic metabolic acidosis with low urinary ammonium excretion rate and inability to decrease urine pH during acidosis, who nevertheless exhibited an intact ability to increase urinary carbon dioxide partial pressure (pCO2) during maximal urine alkalinization and normal ability to acidify the urine after furosemide, suggestive of a gradient-type defect DRTA. This patient had never been exposed to amphotericin B. To our knowledge, this is the first fully documented report of primary DRTA that can be attributed to gradient defect.
Authors:
M Bonilla-Felix
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  American journal of kidney diseases : the official journal of the National Kidney Foundation     Volume:  27     ISSN:  0272-6386     ISO Abbreviation:  Am. J. Kidney Dis.     Publication Date:  1996 Mar 
Date Detail:
Created Date:  1996-05-14     Completed Date:  1996-05-14     Revised Date:  2005-11-17    
Medline Journal Info:
Nlm Unique ID:  8110075     Medline TA:  Am J Kidney Dis     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  428-30     Citation Subset:  IM    
Affiliation:
Division of Pediatric Nephrology, Department of Pediatrics, University of Texas-Health Science Center at Houston, TX 77030, USA.
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MeSH Terms
Descriptor/Qualifier:
Acetazolamide / diagnostic use
Acidosis, Renal Tubular / blood,  diagnosis,  etiology*,  urine
Carbon Dioxide
Diuretics / diagnostic use
Furosemide / diagnostic use
Humans
Hydrogen-Ion Concentration
Infant
Male
Partial Pressure
Time Factors
Chemical
Reg. No./Substance:
0/Diuretics; 124-38-9/Carbon Dioxide; 54-31-9/Furosemide; 59-66-5/Acetazolamide

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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