| Primary biliary cirrhosis associated with mixed type autoimmune hemolytic anemia and sicca syndrome: a case report and review of literature. | |
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MedLine Citation:
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PMID: 9317084 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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A case presenting with an unusual association of primary biliary cirrhosis and mixed type autoimmune hemolytic anemia plus sicca syndrome is described. The 49-yr-old female primary biliary cirrhosis patient had a confirmed sicca syndrome and presented with jaundice and life-threatening anemia. Laboratory tests revealed positive Coombs' test with coexisting cold and warm autoantibodies. She was successfully treated by blood transfusion with packed red cells lacking any red cell antigens corresponding to serum alloantibodies and pulse methylprednisolone therapy. The patient remained stable under maintenance treatment using oral steroids and ursodeoxycholic acid. This case is probably the first reported showing an association between primary biliary cirrhosis and mixed type autoimmune hemolytic anemia plus sicca syndrome and was probably induced by heterogenous and complicated autoimmune reactions. |
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Authors:
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C Y Chen; C L Lu; C F Chiu; F Y Chang; S D Lee |
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Publication Detail:
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Type: Case Reports; Journal Article; Review |
Journal Detail:
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Title: The American journal of gastroenterology Volume: 92 ISSN: 0002-9270 ISO Abbreviation: Am. J. Gastroenterol. Publication Date: 1997 Sep |
Date Detail:
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Created Date: 1997-10-22 Completed Date: 1997-10-22 Revised Date: 2005-11-16 |
Medline Journal Info:
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Nlm Unique ID: 0421030 Medline TA: Am J Gastroenterol Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 1547-9 Citation Subset: IM |
Affiliation:
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Department of Medicine, Veterans General Hospital-Taipei and National Yang-Ming University, Taiwan. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Administration, Oral Anemia, Hemolytic, Autoimmune / complications*, immunology, therapy Anti-Inflammatory Agents / administration & dosage, therapeutic use Antigens / immunology Autoantibodies / analysis Autoimmune Diseases / complications*, immunology, therapy Blood Transfusion Cholagogues and Choleretics / administration & dosage, therapeutic use Erythrocyte Transfusion Erythrocytes / immunology Female Glucocorticoids / administration & dosage, therapeutic use Humans Isoantibodies / immunology Jaundice / etiology Liver Cirrhosis, Biliary / complications*, immunology, therapy Methylprednisolone / administration & dosage, therapeutic use Middle Aged Sjogren's Syndrome / complications*, immunology, therapy Treatment Outcome Ursodeoxycholic Acid / administration & dosage, therapeutic use |
| Chemical | |
Reg. No./Substance:
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0/Anti-Inflammatory Agents; 0/Antigens; 0/Autoantibodies; 0/Cholagogues and Choleretics; 0/Glucocorticoids; 0/Isoantibodies; 128-13-2/Ursodeoxycholic Acid; 83-43-2/Methylprednisolone |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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