Document Detail


Primary antiphospholipid syndrome presented by total infarction of right kidney with nephrotic syndrome.
MedLine Citation:
PMID:  10442498     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We report the case of a young woman with primary antiphospholipid syndrome (APS), which presented with acute renal failure, hypoproteinemia, hypoalbuminemia and nephrotic proteinuria. Investigations showed total infarction of right kidney by extensive arterial and vein thrombosis and presence of anticardiolipin antibodies IgG isotype (anti-beta2-glycoprotein I-positive). She was submitted to right nefrectomy and initiated anticoagulant therapy. After nefrectomy, the postoperative period was marked by the development of arterial hypertension and persistence of nephrotic syndrome. Hypertension was treated with antihypertensive drugs (IECA, beta-blocker and calcium antagonist). As the nephrotic syndrome persisted despite anticoagulant and antihypertensive therapy, the patient was treated with oral corticosteroids. Her renal function improved, hypoproteinemia and hypoalbuminemia corrected to normal values and proteinuria decreased to subnephrotic value. We discuss the unusual presentation of this case of primary antiphospholipid syndrome with total unilateral renal thrombosis and nephrotic syndrome that respond to anticoagulant, antihypertensive and corticosteroid therapy.
Authors:
H Sá; L Freitas; A Mota; F Cunha; A Marques
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  Clinical nephrology     Volume:  52     ISSN:  0301-0430     ISO Abbreviation:  Clin. Nephrol.     Publication Date:  1999 Jul 
Date Detail:
Created Date:  1999-09-28     Completed Date:  1999-09-28     Revised Date:  2005-11-16    
Medline Journal Info:
Nlm Unique ID:  0364441     Medline TA:  Clin Nephrol     Country:  GERMANY    
Other Details:
Languages:  eng     Pagination:  56-60     Citation Subset:  IM    
Affiliation:
Nephrology Department, Hospitais da Universidade de Coimbra, Portugal.
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Adrenal Cortex Hormones / therapeutic use
Antibodies, Anticardiolipin / isolation & purification
Anticoagulants / therapeutic use
Antihypertensive Agents / therapeutic use
Antiphospholipid Syndrome / complications*,  drug therapy,  physiopathology
Female
Humans
Infarction / etiology*
Kidney / blood supply*
Kidney Failure, Acute / etiology
Nephrectomy
Nephrotic Syndrome / etiology*,  physiopathology,  therapy
Renal Artery / radiography
Chemical
Reg. No./Substance:
0/Adrenal Cortex Hormones; 0/Antibodies, Anticardiolipin; 0/Anticoagulants; 0/Antihypertensive Agents

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