Document Detail


Prenatal diagnosis of Schwartz-Jampel syndrome with early manifestation.
MedLine Citation:
PMID:  2646626     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A mother who had given birth to a child with Schwartz-Jampel syndrome (SJS) with neonatal manifestations (myotonia, congenital contractures, bowing of femora and tibiae) underwent ultrasonic fetal examination during the 17th and 19th week of her second pregnancy. Moderately decreased fetal motor activity and constant flexion of the fingers were observed at both examinations. In addition, there was mild bowing and shortening of the femora. At birth, the child presented with the characteristic pattern of SJS similar to her older brother. Prenatal ultrasonic diagnosis of Schwartz-Jampel syndrome is possible, at least for the form with neonatal onset of myotonia and contractures.
Authors:
U A Hunziker; G Savoldelli; E Boltshauser; A Giedion; A Schinzel
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Prenatal diagnosis     Volume:  9     ISSN:  0197-3851     ISO Abbreviation:  Prenat. Diagn.     Publication Date:  1989 Feb 
Date Detail:
Created Date:  1989-04-20     Completed Date:  1989-04-20     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  8106540     Medline TA:  Prenat Diagn     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  127-31     Citation Subset:  IM    
Affiliation:
Department of Pediatrics, University of Zürich, Switzerland.
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MeSH Terms
Descriptor/Qualifier:
Adult
Female
Fetal Movement
Humans
Infant, Newborn
Male
Osteochondrodysplasias / diagnosis*,  genetics
Pregnancy
Prenatal Diagnosis*
Ultrasonography*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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