| Postmenarchal development of chylous ascites in acrocephalosyndactyly with congenital lymphatic dysplasia. | |
| | |
MedLine Citation:
|
PMID: 11336770 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
|
BACKGROUND: Acrocephalosyndactyly is a syndrome characterized by congenital malformation of the skull with craniosynostosis, midface hypoplasia, and symmetrical webbed fusion of the fingers and toes. We describe a possible pathophysiologic mechanism for chylous ascites that developed several months after menarche in a woman with acrocephalosyndactyly and congenital lymphatic dysplasia. CASE: A 25-year-old nulligravid woman with acrocephalosyndactyly, at 18 months after menarche, developed persistent abdominal distension at age 18 years. Laparoscopy at age 25 years revealed chylous ascites with marked chronic peritoneal inflammation, and lymphatic dysplasia with lymphocysts. With hormone manipulation, the chylous ascites fluctuated. CONCLUSION: After menarche in a woman with acrocephalosyndactyly, ovarian steroid hormones might have increased lymph production and hydrostatic pressure, causing rupture of congenitally dysplastic lymph vessels resulting in chylous ascites. |
| | |
Authors:
|
R E Batt; S R Michalski; T Mahl; J C Reynhout |
Publication Detail:
|
Type: Case Reports; Journal Article |
Journal Detail:
|
Title: Obstetrics and gynecology Volume: 97 ISSN: 0029-7844 ISO Abbreviation: Obstet Gynecol Publication Date: 2001 May |
Date Detail:
|
Created Date: 2001-05-04 Completed Date: 2001-05-24 Revised Date: 2009-10-26 |
Medline Journal Info:
|
Nlm Unique ID: 0401101 Medline TA: Obstet Gynecol Country: United States |
Other Details:
|
Languages: eng Pagination: 829-31 Citation Subset: AIM; IM |
Affiliation:
|
Department of Gynecology-Obstetrics, State University of New York at Buffalo, 5648 Broadway, Buffalo, NY 14086-2317, USA. ronbatt@localnet.com |
Export Citation:
|
APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
|
Acrocephalosyndactylia
/
complications* Adult Chylous Ascites / complications, diagnosis*, diet therapy Diagnosis, Differential Female Humans Lymphatic Diseases / complications*, congenital Menarche |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
Previous Document: Acute peritonitis due to introital stenosis and perforation of a bowel neovagina in a transsexual.
Next Document: Compartment syndrome associated with lithotomy position and intermittent compression stockings.