Document Detail


Polysplenia with pulmonary arteriovenous malformations.
MedLine Citation:
PMID:  8469631     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A patient with polysplenia syndrome, dextrocardia, left atrial isomerism, normal great vessel relationships, and no intracardiac shunts developed progressive cyanosis and clubbing. Pulmonary arteriovenous malformations (PAVMs) were diagnosed by angiography and confirmed by lung biopsy. Superior mesenteric arteriogram revealed hypoplasia of the intrahepatic portal vein branches and a portosystemic shunt. The possible etiologies of PAVMs are discussed.
Authors:
J Papagiannis; R J Kanter; E L Effman; P C Pratt; R Marcille; I B Browning; B E Armstrong
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Pediatric cardiology     Volume:  14     ISSN:  0172-0643     ISO Abbreviation:  Pediatr Cardiol     Publication Date:  1993 Mar 
Date Detail:
Created Date:  1993-05-07     Completed Date:  1993-05-07     Revised Date:  2008-02-20    
Medline Journal Info:
Nlm Unique ID:  8003849     Medline TA:  Pediatr Cardiol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  127-9     Citation Subset:  IM    
Affiliation:
Department of Pediatrics, Duke University Medical Center, Durham, NC 27710.
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MeSH Terms
Descriptor/Qualifier:
Arteriovenous Malformations / diagnosis*,  pathology
Biopsy
Child, Preschool
Female
Heart Defects, Congenital / diagnosis*,  pathology
Humans
Liver / pathology
Lung / pathology
Pulmonary Artery / abnormalities*,  pathology
Spleen / abnormalities*
Syndrome

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