| Polysplenia syndrome with agenesis of the dorsal pancreas and preduodenal portal vein presenting with obstructive jaundice--a case report and literature review. | |
| | |
MedLine Citation:
|
PMID: 22011826 Owner: NLM Status: In-Data-Review |
Abstract/OtherAbstract:
|
Polysplenia, as part of the heterotaxy syndrome, is a rare embryological disorder which results from failure of development of the usual left-right asymmetry of organs. It is often associated with cardiac and biliary abnormalities, which are the usual causes of death in early neonatal life. A congenitally short pancreas and abnormalities with portal vein formation, gut malrotations and inferior vena cava anomalies are known to be associated with this rare syndrome. We report a case of polysplenia in an adult female presenting with obstructive jaundice owing to choledocholithiasis, possibly formed by biliary stasis as a result of compression of the common bile duct by the preduodenal portal vein, and review the literature. The patient was also found to have complete agenesis of the dorsal pancreas on CT and endoscopic retrograde cholangiopancreatography. |
| | |
Authors:
|
J P Low; D Williams; J R Chaganti |
Related Documents
:
|
4425416 - Early cholecystectomy for acute cholecystitis. 6267526 - Reciprocal antagonism between acth1-24 and beta-endorphin in rats. 2329796 - Hyperacusis and otitis media in individuals with williams syndrome. 1263326 - Intermittent bladder paresis in the pseudoclaudication syndrome. 18406746 - Premenstrual syndrome. 11201226 - Medicinal foodstuffs. xxi. structures of new cucurbitane-type triterpene glycosides, go... |
Publication Detail:
|
Type: Journal Article |
Journal Detail:
|
Title: The British journal of radiology Volume: 84 ISSN: 1748-880X ISO Abbreviation: Br J Radiol Publication Date: 2011 Nov |
Date Detail:
|
Created Date: 2011-10-20 Completed Date: - Revised Date: - |
Medline Journal Info:
|
Nlm Unique ID: 0373125 Medline TA: Br J Radiol Country: England |
Other Details:
|
Languages: eng Pagination: 217-20 Citation Subset: AIM; IM |
Affiliation:
|
Department of Radiology. |
Export Citation:
|
APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
|
|
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
Previous Document: Synovial chondromatosis in the temporomandibular joint: a case with typical imaging features and pat...
Next Document: Subcutaneous calcification in the pectoralis major flap: a late complication of radiotherapy.