Document Detail


Podocyte phenotypes as defined by expression and distribution of GLEPP1 in the developing glomerulus and in nephrotic glomeruli from MCD, CNF, and FSGS. A dedifferentiation hypothesis for the nephrotic syndrome.
MedLine Citation:
PMID:  9639039     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Glomerular epithelial protein 1 (GLEPP1) is a podocyte receptor membrane protein tyrosine phosphatase located on the apical cell membrane of visceral glomerular epithelial cell (VGEC) foot processes. Double label immunofluorescence, immunoelectron microscopy, and peroxidase immunohistochemistry were used to map the GLEPP1 distribution in the developing glomerulus and in minimal-change nephropathy (MCN), congenital nephrotic syndrome of the Finnish type, and focal-segmental glomerulosclerosis (FSGS). In MCN GLEPP1 was shifted away from the glomerular basement membrane on the apical cell membrane of effaced foot processes. These data are compatible with the previously suggested concept that MCN can be considered a form of dedifferentiation of the podocyte phenotype. Similarly, changes seen in congenital nephrotic syndrome of the Finnish type can be considered a consequence of failure to complete normal podocyte development. In FSGS glomeruli GLEPP1 was frequently absent from VGECs, even when no sclerosis was detectable in that glomerulus. Therefore, in FSGS, VGECs may lose GLEPP1, and this loss appears to occur in the absence of scarring and may, therefore, precede the scarring process. We speculate that a changed VGEC phenotype that does not express GLEPP1 might have properties similar to the early undifferentiated VGEC developmental phenotype. GLEPP1 distribution pattern and absence from glomeruli of individuals with nephrotic syndrome may, therefore, represent a useful phenotypic marker.
Authors:
K Sharif; M Goyal; D Kershaw; R Kunkel; R Wiggins
Related Documents :
21218389 - Descemet stripping automated endothelial keratoplasty combined with phacoemulsification...
17995529 - Pathogenesis of oedema in nephrotic syndrome: role of epithelial sodium channel.
1580319 - Case report: nephrotic syndrome associated with a total hydatidiform mole.
11685439 - Superior sagittal sinus thrombosis: a rare complication in a child with nephrotic syndr...
9569959 - A case of guillain-barré syndrome developed minimal change nephrotic syndrome simultan...
421189 - Retroperitoneal paraganglioma and systemic amyloidosis: a case report.
14710969 - Primary sjogren's syndrome: rarity in india.
18661429 - Insulin resistance and metabolic syndrome in chronic liver diseases: old entities with ...
22390119 - Tako-tsubo like syndrome triggered by meperidine.
Publication Detail:
Type:  Journal Article; Research Support, U.S. Gov't, P.H.S.    
Journal Detail:
Title:  Experimental nephrology     Volume:  6     ISSN:  1018-7782     ISO Abbreviation:  Exp. Nephrol.     Publication Date:    1998 May-Jun
Date Detail:
Created Date:  1998-08-17     Completed Date:  1998-08-17     Revised Date:  2007-11-15    
Medline Journal Info:
Nlm Unique ID:  9302239     Medline TA:  Exp Nephrol     Country:  SWITZERLAND    
Other Details:
Languages:  eng     Pagination:  234-44     Citation Subset:  IM    
Affiliation:
Department of Internal Medicine, University of Michigan, Ann Arbor, USA.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Animals
Animals, Newborn
Antibodies, Monoclonal
Biological Markers
Fluorescent Antibody Technique
Glomerulosclerosis, Focal Segmental / metabolism,  pathology*
Humans
Immunoenzyme Techniques
Immunophenotyping
Kidney Glomerulus / chemistry*,  embryology*,  ultrastructure
Membrane Proteins / analysis*,  genetics,  immunology
Mice
Microscopy, Immunoelectron
Nephrosis, Lipoid / metabolism,  pathology
Nephrotic Syndrome / metabolism,  pathology*
Phenotype
Protein Tyrosine Phosphatases / analysis*,  genetics,  immunology
Rabbits
Receptor-Like Protein Tyrosine Phosphatases, Class 3
Grant Support
ID/Acronym/Agency:
DK39255/DK/NIDDK NIH HHS; DK46073/DK/NIDDK NIH HHS
Chemical
Reg. No./Substance:
0/Antibodies, Monoclonal; 0/Biological Markers; 0/Membrane Proteins; EC 3.1.3.48/PTPRO protein, human; EC 3.1.3.48/Protein Tyrosine Phosphatases; EC 3.1.3.48/Ptpro protein, mouse; EC 3.1.3.48/Receptor-Like Protein Tyrosine Phosphatases, Class 3

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  The renal TGF-beta system in the db/db mouse model of diabetic nephropathy.
Next Document:  Renal hemodynamic response to erythropoietin-induced polycythemia in 5/6 nephrectomised rats is diff...