Document Detail


Pheochromocytoma storm presenting as cardiovascular collapse at term pregnancy.
MedLine Citation:
PMID:  15580162     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Pheochromocytomas are neuroendocrine tumors that typically present with paroxysms of hypertension, but occasionally can lead to marked hemodynamic instability, left ventricular dysfunction, and cardiovascular collapse. Although pheochromocytoma in pregnancy is rare, factors specific to pregnancy can precipitate catecholamine crisis, making diagnosis and treatment challenging. We present a case of acute cardiovascular collapse with transient left ventricular dysfunction due to catecholamine crisis in a healthy young woman at term pregnancy. Further clinical and genetic investigation revealed pheochromocytoma as part of multiple endocrine neoplasia IIa (Sipple syndrome). A discussion of diagnosis and treatment strategies for pheochromocytoma in pregnancy and acute catecholamine crisis accompanies this report.
Authors:
Alexander Langerman; John A Schneider; R Parker Ward
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Reviews in cardiovascular medicine     Volume:  5     ISSN:  1530-6550     ISO Abbreviation:  Rev Cardiovasc Med     Publication Date:  2004  
Date Detail:
Created Date:  2004-12-06     Completed Date:  2005-01-18     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  100960007     Medline TA:  Rev Cardiovasc Med     Country:  United States    
Other Details:
Languages:  eng     Pagination:  226-30     Citation Subset:  IM    
Affiliation:
Section of Cardiology, Department of Medicine, University of Chicago, Chicago, Illinois, USA.
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MeSH Terms
Descriptor/Qualifier:
Acute Disease
Adrenal Gland Neoplasms / diagnosis*
Adult
Cardiovascular Diseases / diagnosis*,  etiology,  therapy
Female
Humans
Multiple Endocrine Neoplasia Type 2a / diagnosis*
Pheochromocytoma / diagnosis*
Pregnancy
Pregnancy Complications, Cardiovascular / diagnosis,  therapy
Pregnancy Complications, Neoplastic / diagnosis*
Ventricular Dysfunction, Left / diagnosis,  etiology,  therapy

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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