Document Detail


Pheochromocytoma and medullary thyroid carcinoma in a pregnant multiple endocrine neoplasia-2A patient.
MedLine Citation:
PMID:  20672905     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
OBJECTIVE: We describe a rare combination of pheochromocytoma and medullary thyroid carcinoma (MTC) during pregnancy.
METHODS: Twenty-three-years old lady, primigravida, was detected to be hypertensive at 12 weeks of gestation and was found to have left adrenal mass on routine obstetric scan. She had a goitre on examination which was proven to be MTC on fine needle aspiration cytology. Twenty-four hours urinary vanillyl mandelic acid and serum calcitonin levels were elevated. After adequate α and β blockade she underwent left adrenalectomy during second trimester of gestation with no significant perioperative complications. Twelve days later she underwent total thyroidectomy.
RESULTS: Adrenal mass was confirmed to be pheochromocytoma while MTC was confirmed in the thyroidectomy specimen. Post-operatively, she was normotensive and delivered a healthy female baby at term. Both mother and the baby tested positive for germline RET mutation (C634W) in exon 11.
CONCLUSION: We describe a rare case of pregnant multiple endocrine neoplasia-2A patient with pheochromocytoma and MTC.
Authors:
Vijaya Sarathi; Tushar R Bandgar; Padma S Menon; Nalini S Shah
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Publication Detail:
Type:  Case Reports; Journal Article     Date:  2010-07-30
Journal Detail:
Title:  Gynecological endocrinology : the official journal of the International Society of Gynecological Endocrinology     Volume:  27     ISSN:  1473-0766     ISO Abbreviation:  Gynecol. Endocrinol.     Publication Date:  2011 Aug 
Date Detail:
Created Date:  2011-07-05     Completed Date:  2011-12-05     Revised Date:  2012-06-04    
Medline Journal Info:
Nlm Unique ID:  8807913     Medline TA:  Gynecol Endocrinol     Country:  England    
Other Details:
Languages:  eng     Pagination:  533-5     Citation Subset:  IM    
Affiliation:
Department of Endocrinology, Seth G S Medical College and KEM Hospital, Mumbai, Maharashtra, India. drvijayasarathi@gmail.com
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MeSH Terms
Descriptor/Qualifier:
Adrenal Gland Neoplasms / diagnosis*,  genetics,  physiopathology,  surgery
Adult
Amino Acid Substitution
Carcinoma, Medullary / diagnosis*,  genetics,  physiopathology,  surgery
Female
Humans
Hypertension, Pregnancy-Induced / etiology
Live Birth
Multiple Endocrine Neoplasia Type 2a / diagnosis*,  genetics,  physiopathology,  surgery
Mutation
Pheochromocytoma / diagnosis*,  genetics,  physiopathology,  surgery
Pregnancy
Pregnancy Complications, Neoplastic / diagnosis*,  genetics,  physiopathology,  surgery
Pregnancy Trimester, First
Proto-Oncogene Proteins c-ret / genetics
Thyroid Neoplasms / diagnosis*,  genetics,  physiopathology,  surgery
Young Adult
Chemical
Reg. No./Substance:
EC 2.7.10.1/Proto-Oncogene Proteins c-ret; EC 2.7.10.1/RET protein, human

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