Document Detail


Pheochromocytoma and Tetralogy of Fallot: A Rare but Potentially Dangerous Combination.
MedLine Citation:
PMID:  24449673     Owner:  NLM     Status:  Publisher    
Abstract/OtherAbstract:
Objective: To describe a case of Pheochromocytoma (PHEO) with Tetralogy of Fallot and discuss the difficulties encountered during the management of this patient with review of the literature.Method: We report the clinical course, imaging, and management issues of our patient and review relevant literature.Result: A 14 years female who is a known case of Tetralogy of Fallot presented with classical paroxysmal symptoms and worsening of dyspnoea. She was diagnosed to have an epinephrine secreting PHEO based on biochemical, radiological and functional imaging. She was treated with an α-1 blocker for control of paroxysms but developed a severe cyanotic spells. She required addition of a calcium channel blocker for control of paroxysms and underwent successful cardiac repair.Conclusion: Treatment of combination of cyanotic congenital heart disease (CCHD) and PHEO requires an individualised and multidisciplinary approach with judicious use of available medications. This is the first case of uncorrected TOF and epinephrine secreting PHEO. Our case also reiterates the need of further studies to better understand the pathophysiological link between PHEO/PGL and CCHD.
Authors:
Rajeev Kasaliwal; Vijaya Sarathi; Reshma Pandit; Sweta R Budyal; Amol Bukan; Harshal Kakade; Varsha S Jagtap; Anurag R Lila; Varsha S Jagtap; Anurag R Lila; Tushar Bandgar; Padmavathy S Menon; Nalini S Shah
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Publication Detail:
Type:  JOURNAL ARTICLE     Date:  2014-1-21
Journal Detail:
Title:  Endocrine practice : official journal of the American College of Endocrinology and the American Association of Clinical Endocrinologists     Volume:  -     ISSN:  1934-2403     ISO Abbreviation:  Endocr Pract     Publication Date:  2014 Jan 
Date Detail:
Created Date:  2014-1-22     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9607439     Medline TA:  Endocr Pract     Country:  -    
Other Details:
Languages:  ENG     Pagination:  1-15     Citation Subset:  -    
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