| Persistent mullerian duct syndrome and transverse testicular ectopia: embryology, presentation, and management. | |
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MedLine Citation:
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PMID: 18082721 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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BACKGROUND: The finding of persistent mullerian duct syndrome (PMDS) with transverse testicular ectopia (TTE) is rare. We present nonidentical triplets with PMDS with TTE. CASES: Triplet A presented with a right inguinal hernia and left nonpalpable testis at 4 months of age. Ultrasound demonstrated 1 testis in the right hemiscrotum. Laparoscopy revealed both testes in the right inguinal canal with a thick midline structure. Triplet B presented at 6 months of age in the exact manner with similar intraoperative findings as triplet A. No additional mullerian structures were identified in triplets A and B. Both underwent laparoscopic left orchiopexy and open right inguinal herniorraphy/orchiopexy. A portion of vas was noted in the path specimen of triplet B. Triplet C presented at 7 months of age with a nonpalpable left testis. Laparoscopy demonstrated bilateral fallopian tubes and a midline uterine remnant. Open bilateral orchiopexy was performed, and bilateral biopsies confirmed testes. All 3 were 46-X,Y. CONCLUSION: Persistent mullerian duct syndrome with TTE may be encountered when performing laparoscopy for patients with nonpalpable testis. The persistent mullerian remnants vary among individuals and alter the normal anatomy, thus may complicate diagnosis and surgical management. |
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Authors:
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Melanie Wuerstle; Timothy Lesser; Richard Hurwitz; Harry Applebaum; Steven L Lee |
Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Journal of pediatric surgery Volume: 42 ISSN: 1531-5037 ISO Abbreviation: J. Pediatr. Surg. Publication Date: 2007 Dec |
Date Detail:
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Created Date: 2007-12-17 Completed Date: 2008-01-22 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 0052631 Medline TA: J Pediatr Surg Country: United States |
Other Details:
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Languages: eng Pagination: 2116-9 Citation Subset: IM |
Affiliation:
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Division of Pediatric Surgery and Department of Urology, Kaiser Permanente, Los Angeles Medical Center, Los Angeles, CA 90027, USA. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Abnormalities, Multiple
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diagnosis,
surgery Choristoma / diagnosis*, surgery Combined Modality Therapy Cryptorchidism / diagnosis*, embryology, surgery Follow-Up Studies Hernia, Inguinal / congenital, diagnosis*, surgery Humans Infant Laparotomy Male Mullerian Ducts / abnormalities*, embryology, surgery Syndrome Testis* Treatment Outcome Triplets Urologic Surgical Procedures, Male / methods |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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