Document Detail


Permanent t-tube insertion in two patients with Hurler's syndrome.
MedLine Citation:
PMID:  17365060     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Hearing loss in mucopolysaccharidosis is usually both conductive and sensorineural. The conductive component is attributable to serous otitis media secondary to dysfunction of the eustachian tube and chronic thickening of the mucosa of the middle ear. The conductive component may persist after myringotomy and insertion of short-term or long-term ventilation tubes. In Hurler's syndrome, death usually occurs in the first decade of life. In our study, we present two cases, a three-year-old girl and a four-year-old boy, who were diagnosed with Hurler's syndrome. Both children have a history of otitis media with effusion requiring repeated short-term ventilation tube insertions that were unsuccessful. Permanent t-tubes were inserted in both cases. Results showed an approximate 20 dB improvement in hearing sensitivity postoperatively for each patient.
Authors:
Fatih Oghan; Ugur Harputluoglu; Ender Guclu; Ali Guvey; Nursen Turan; Ozcan Ozturk
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  International journal of audiology     Volume:  46     ISSN:  1499-2027     ISO Abbreviation:  Int J Audiol     Publication Date:  2007 Feb 
Date Detail:
Created Date:  2007-03-16     Completed Date:  2007-06-12     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101140017     Medline TA:  Int J Audiol     Country:  England    
Other Details:
Languages:  eng     Pagination:  94-6     Citation Subset:  IM    
Affiliation:
Council of Forensic Medicine, ENT Department, Istanbul, Turkey. fatihoghan@hotmail.com
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MeSH Terms
Descriptor/Qualifier:
Acoustic Impedance Tests
Child, Preschool
Disease Progression
Evoked Potentials, Auditory, Brain Stem / physiology
Female
Humans
Male
Middle Ear Ventilation / instrumentation,  methods*
Mucopolysaccharidoses / complications
Mucopolysaccharidosis I / surgery*
Otitis Media with Effusion / complications,  surgery*
Prosthesis Design
Severity of Illness Index

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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