| Peripartum management of two parturients with ornithine transcarbamylase deficiency. | |
| | |
MedLine Citation:
|
PMID: 22138526 Owner: NLM Status: Publisher |
Abstract/OtherAbstract:
|
Ornithine transcarbamylase deficiency is a rare X-linked disorder in which female carriers are usually heterozygous for the ornithine transcarbamylase deficiency gene. In pregnancy it has been associated with altered mental status, seizures, coma and death, especially in the postpartum period. We report the management of labor and delivery in two parturients with known ornithine transcarbamylase deficiency. Both patients were maintained on arginine, citrulline and sodium phenylacetate therapy with restricted protein intake during pregnancy. Neuraxial techniques were used for pain relief in labor and anesthesia for operative delivery. A dextrose infusion provided caloric intake during labor and perioperatively. |
| | |
Authors:
|
U Ituk; O C Constantinescu; T K Allen; M J Small; A S Habib |
Related Documents
:
|
472816 - Cervical cerclage: twenty years' experience. 3486266 - The technique of fibrin adhesion for premature rupture of the membranes during pregnancy. 10844796 - Spinal angulation after anterior discectomy and graftless fusion. 12128266 - Management and evolution of cervical intraepithelial neoplasia during pregnancy and pos... 1837946 - Congenital urethral diverticulum in the male: a twenty-one year old man with a congenit... 21211836 - Review: fetal antigens--identity, origins, and influences on the maternal immune system. |
Publication Detail:
|
Type: JOURNAL ARTICLE Date: 2011-12-2 |
Journal Detail:
|
Title: International journal of obstetric anesthesia Volume: - ISSN: 1532-3374 ISO Abbreviation: - Publication Date: 2011 Dec |
Date Detail:
|
Created Date: 2011-12-5 Completed Date: - Revised Date: - |
Medline Journal Info:
|
Nlm Unique ID: 9200430 Medline TA: Int J Obstet Anesth Country: - |
Other Details:
|
Languages: ENG Pagination: - Citation Subset: - |
Copyright Information:
|
Copyright © 2011 Elsevier Ltd. All rights reserved. |
Affiliation:
|
Department of Anesthesiology, Duke University Health System, Durham NC, USA. |
Export Citation:
|
APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
|
|
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
Previous Document: Type A aortic dissection in pregnancy.
Next Document: Binocular fusion of luminance, color, motion and flicker - Two eyes are worse than one.