Document Detail

Perioral myoclonia with absences? A case report with EEG and voltage mapping analysis.
MedLine Citation:
PMID:  9253489     Owner:  NLM     Status:  MEDLINE    
The author presents clinical and electroencephalographic data of an epileptic girl, whose absences started at the age of 2. Based on seizure semiology, serial EEG and video-EEG recording, 7 years of follow-up and other clinical data, the patient was diagnosed as having the PMA ('perioral myoclonus with absences') syndrome. There were some disagreement between clinical and EEG data, however. Finally, she became completely seizure free on valproate+lamotrigine medication. Detailed EEG and voltage mapping analysis disclosed that spike movements of ictal and interictal generalized spike-wave discharges showed always the same, very consistent, peculiar topographic pattern. This pattern was fundamentally different from spike patterns associated with typical absence seizures (recorded in other patients). Analysis of clinical, EEG and voltage mapping results-suggest that actually this case might be rather classified as myoclonic epilepsy. The conjunction of this case to the PMA syndrome has been discussed.
B Clemens
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Brain & development     Volume:  19     ISSN:  0387-7604     ISO Abbreviation:  Brain Dev.     Publication Date:  1997 Jul 
Date Detail:
Created Date:  1997-10-01     Completed Date:  1997-10-01     Revised Date:  2013-08-21    
Medline Journal Info:
Nlm Unique ID:  7909235     Medline TA:  Brain Dev     Country:  NETHERLANDS    
Other Details:
Languages:  eng     Pagination:  353-8     Citation Subset:  IM    
County Hospital, Neurological Department, Debrecen, Hungary.
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MeSH Terms
Anticonvulsants / administration & dosage
Brain Mapping*
Epilepsy, Absence / complications,  drug therapy,  physiopathology*
Myoclonus / complications,  drug therapy,  physiopathology*
Triazines / administration & dosage
Video Recording
Reg. No./Substance:
0/Anticonvulsants; 0/Triazines; U3H27498KS/lamotrigine

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

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