Document Detail


Pediatric nephrotic syndrome: from the simple to the complex.
MedLine Citation:
PMID:  19615560     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Remarkable advances have been made in the past decade in understanding the pathophysiology of idiopathic nephrotic syndrome. Although the initiating events leading to the onset of proteinuria still are not well defined, it has become increasingly clear that many glomerular diseases can be classified as podocytopathies, with injury to the podocyte playing a major role in the development and progression of disease. A complex interaction of immune system mediators, slit diaphragm signal transduction, podocyte injury and conformational change, and mediators of apoptosis and fibrosis determine the extent and nature of proteinuria and progression of glomerulosclerosis. New insights into the pathogenesis of idiopathic nephrotic syndrome likely will lead to innovative therapies and new approaches to management and prevention.
Authors:
Jerome C Lane; Frederick J Kaskel
Publication Detail:
Type:  Journal Article; Review    
Journal Detail:
Title:  Seminars in nephrology     Volume:  29     ISSN:  1558-4488     ISO Abbreviation:  Semin. Nephrol.     Publication Date:  2009 Jul 
Date Detail:
Created Date:  2009-07-20     Completed Date:  2009-09-22     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8110298     Medline TA:  Semin Nephrol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  389-98     Citation Subset:  IM    
Affiliation:
Division of Kidney Diseases, Department of Pediatrics, Children's Memorial Hospital, 2300 Children's Plaza, Chicago, IL 60614, USA. j-lane@northwestern.edu
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MeSH Terms
Descriptor/Qualifier:
Child
Child, Preschool
Disease Progression
Glomerulosclerosis, Focal Segmental / complications*,  genetics,  physiopathology
Humans
Intracellular Signaling Peptides and Proteins / genetics,  metabolism,  physiology
Membrane Proteins / genetics,  metabolism,  physiology
Nephrosis, Lipoid / complications*,  genetics,  physiopathology
Nephrotic Syndrome / genetics,  pathology,  physiopathology*
Podocytes / pathology
Proteinuria / physiopathology
Signal Transduction / genetics
Chemical
Reg. No./Substance:
0/Intracellular Signaling Peptides and Proteins; 0/Membrane Proteins; 0/NPHS2 protein; 0/nephrin

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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