Document Detail


Pathology of angiodysplasia in Klippel-Trenaunay syndrome.
MedLine Citation:
PMID:  2851776     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Klippel-Trenaunay syndrome is a congenital angiodysplasia consisting of the triad of angiomas, osteohypertrophy and venous varicosities. Visceral involvement is not uncommon and may cause life-threatening complications. Presented here is a detailed study of the pathology of angiodysplasia in Klippel-Trenaunay syndrome. Venous fibromuscular dysplasia is the most prominent and consistent vascular lesion other than the cavernous hemangioma which is not unique to this syndrome. Dysplastic veins may also have deformed, insufficient, or absent valves. No agenesis or atresia of the deep veins is found in this series of patients.
Authors:
J T Lie
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Pathology, research and practice     Volume:  183     ISSN:  0344-0338     ISO Abbreviation:  Pathol. Res. Pract.     Publication Date:  1988 Nov 
Date Detail:
Created Date:  1989-03-14     Completed Date:  1989-03-14     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  7806109     Medline TA:  Pathol Res Pract     Country:  GERMANY, WEST    
Other Details:
Languages:  eng     Pagination:  747-55     Citation Subset:  IM    
Affiliation:
Division of Pathology, Mayo Clinic, Rochester, Minnesota.
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Adult
Angiography
Angiomatosis / pathology*
Arteries / abnormalities*
Child
Child, Preschool
Extremities / radiography
Female
Humans
Infant
Klippel-Trenaunay-Weber Syndrome / pathology*
Male
Middle Aged
Veins / abnormalities*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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