Document Detail


Pathogenesis of Kawasaki disease.
MedLine Citation:
PMID:  21447126     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Kawasaki disease (KD) most frequently affects infants and young children under 5 years of age. This disease is considered a kind of systemic vasculitis syndrome, and primarily invades the medium-sized muscular arteries, including coronary arteries. Diagnosis of KD is based on characteristic clinical signs and symptoms, which are classified as principal clinical findings and other clinical and laboratory findings. Even though the aetiology of KD is unknown, epidemiological data suggest that some kinds of infectious agents are involved in the onset of KD. In addition, the data indicate that host genetics underlie the disease's pathogenesis. Histologically, coronary arteritis begins 6-8 days after the onset of KD, and leads immediately to inflammation of all layers of the artery. The inflammation spreads completely around the artery; as a result, structural components of the artery undergo intense damage; the artery then begins to dilate. Inflammatory cell infiltration continues until about the 25th day of the disease, after which the inflammatory cells gradually decrease in number. KD arteritis is characterized by granulomatous inflammation that consists of severe accumulation of monocytes/macrophages. Aberrant activation of monocytes/macrophages is thought to be involved in the formation of vascular lesions. The lesions in all the arteries are relatively synchronous as they evolve from acute to chronic injury. There is no fibrinoid necrosis nor any mixture of acute inflammatory lesions and scarring lesions, which are characteristics in polyarteritis nodosa in KD.
Authors:
K Takahashi; T Oharaseki; Y Yokouchi
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Publication Detail:
Type:  Journal Article; Review    
Journal Detail:
Title:  Clinical and experimental immunology     Volume:  164 Suppl 1     ISSN:  1365-2249     ISO Abbreviation:  Clin. Exp. Immunol.     Publication Date:  2011 May 
Date Detail:
Created Date:  2011-03-30     Completed Date:  2011-04-27     Revised Date:  2012-05-01    
Medline Journal Info:
Nlm Unique ID:  0057202     Medline TA:  Clin Exp Immunol     Country:  England    
Other Details:
Languages:  eng     Pagination:  20-2     Citation Subset:  IM    
Copyright Information:
© 2011 The Authors;Clinical and Experimental Immunology © 2011 British Society for Immunology.
Affiliation:
Department of Pathology, Toho University Ohashi Medical Center, Tokyo, Japan. keitak@oha.toho-u.ac.jp
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MeSH Terms
Descriptor/Qualifier:
Acute Disease
Chronic Disease
Cicatrix / immunology
Coronary Artery Disease / etiology,  immunology*,  pathology
Humans
Immunoglobulins, Intravenous / therapeutic use
Immunologic Factors / therapeutic use
Macrophage Activation / immunology
Macrophages / immunology
Mucocutaneous Lymph Node Syndrome / complications,  immunology*,  pathology,  therapy
Polyarteritis Nodosa / immunology
Chemical
Reg. No./Substance:
0/Immunoglobulins, Intravenous; 0/Immunologic Factors

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