Document Detail


Pancreatic cysts causing biliary obstruction in von Hippel Lindau syndrome.
MedLine Citation:
PMID:  18469445     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
CONTEXT: Extrahepatic biliary obstruction secondary to pancreatic cysts is rare in patients with von Hippel Lindau syndrome. We describe a patient with von Hippel Lindau syndrome who had biliary obstruction due to pancreatic cysts who was initially managed endoscopically and then surgically. CASE REPORT: A female patient with von Hippel Lindau syndrome which had been diagnosed ten years earlier based on the presence of pancreatic and renal cysts with retinal hemangiomas, presented with cholestatic jaundice of two months duration. On investigation, she was found to have lower end biliary obstruction caused by pancreatic cysts. The patient was initially managed with endoscopic retrograde cholangiography and a 7 French/10F/12F biliary plastic stent placement. Her cholestatic symptoms improved but required frequent stent exchange due to stent block; she finally underwent a hepaticojejunostomy and is doing well on follow-up. CONCLUSION: This case highlights the fact that pancreatic involvement leading to biliary obstruction, although uncommon, can occur in patients with von Hippel Lindau syndrome. Endoscopic biliary stent placement and surgery are helpful in these patients.
Authors:
Rahul Gupta; Deepak Chettri; Arun Sharma; Ajay Duseja; Radha Krishan Dhiman; Yogesh Kumar Chawla; Naveen Kalra; Amod Gupta; Arunanshu Behera
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Publication Detail:
Type:  Case Reports; Journal Article     Date:  2008-05-08
Journal Detail:
Title:  JOP : Journal of the pancreas     Volume:  9     ISSN:  1590-8577     ISO Abbreviation:  JOP     Publication Date:  2008  
Date Detail:
Created Date:  2008-05-12     Completed Date:  2008-07-22     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101091810     Medline TA:  JOP     Country:  Italy    
Other Details:
Languages:  eng     Pagination:  313-6     Citation Subset:  IM    
Affiliation:
Department of Hepatology, Postgraduate Institute of Medical Education and Research, Chandigarh, India.
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MeSH Terms
Descriptor/Qualifier:
Adult
Cholestasis / etiology*,  surgery
Female
Hemangioma / complications,  diagnosis
Humans
Jaundice, Obstructive / etiology
Pancreatic Cyst / complications*,  surgery
Retinal Neoplasms / complications,  diagnosis
von Hippel-Lindau Disease / complications*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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