Document Detail


POEMS syndrome and Waldenström's macroglobulinaemia.
MedLine Citation:
PMID:  8655693     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A 58 year old man presented with a three year history of impotence, night sweats and ankle swelling. On examination, the patient fulfilled the diagnostic criteria for POEMS syndrome, but was unusual in that he also had underlying Waldenström's macroglobulinaemia with IgM kappa paraproteinaemia. The patient was treated with intermittent chlorambucil and made a good recovery. POEMS syndrome has been described in association with osteosclerotic myeloma and Castleman's disease. The paraprotein involved is usually IgG or IgA with lambda light chains. This case indicates that the presence of lambda light chains is not essential for the pathogenesis of POEMS syndrome. It also emphasises the diversity of plasma cell dyscrasias that can manifest as POEMS syndrome.
Authors:
S R Pavord; P T Murphy; V E Mitchell
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of clinical pathology     Volume:  49     ISSN:  0021-9746     ISO Abbreviation:  J. Clin. Pathol.     Publication Date:  1996 Feb 
Date Detail:
Created Date:  1996-07-31     Completed Date:  1996-07-31     Revised Date:  2009-11-18    
Medline Journal Info:
Nlm Unique ID:  0376601     Medline TA:  J Clin Pathol     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  181-2     Citation Subset:  AIM; IM    
Affiliation:
Department of Haematology, Leicester Royal Infirmary.
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MeSH Terms
Descriptor/Qualifier:
Humans
Immunoglobulin M / blood*
Immunoglobulin kappa-Chains / blood*
Male
Middle Aged
POEMS Syndrome / etiology*
Paraproteinemias / complications*
Waldenstrom Macroglobulinemia / complications*
Chemical
Reg. No./Substance:
0/Immunoglobulin M; 0/Immunoglobulin kappa-Chains
Comments/Corrections

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