| Overall management of patients with Dravet syndrome. | |
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MedLine Citation:
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PMID: 21504428 Owner: NLM Status: In-Process |
Abstract/OtherAbstract:
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Dravet syndrome, or as it was called in the past 'severe myoclonic epilepsy in infancy', is a drug-resistant epilepsy first described by Charlotte Dravet in 1978. Besides the well-known and well-described therapy resistance, Dravet syndrome dramatically impacts the development and behaviour of the affected children. As it is still not a curable disease, families need to be taught how to cope with the disorder and will require assistance from both clinical and non-clinical structures. At the onset of the disease, many questions arise regarding the diagnosis of Dravet syndrome, the severity of the illness and its deleterious effects, and the management of seizures, especially the long-lasting status epilepticus. Once the diagnosis has been established, severe convulsions, often unpredictable and long-lasting, are still a major worry, but developmental and behavioural problems also rapidly become a serious concern. Later on, nearly all parents will have a child who becomes an adult with special needs, requiring specialised attention from professionals. |
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Authors:
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Berten Ceulemans |
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Publication Detail:
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Type: Journal Article |
Journal Detail:
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Title: Developmental medicine and child neurology Volume: 53 Suppl 2 ISSN: 1469-8749 ISO Abbreviation: Dev Med Child Neurol Publication Date: 2011 Apr |
Date Detail:
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Created Date: 2011-04-20 Completed Date: - Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 0006761 Medline TA: Dev Med Child Neurol Country: England |
Other Details:
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Languages: eng Pagination: 19-23 Citation Subset: IM |
Copyright Information:
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© 2011 The Authors. Developmental Medicine & Child Neurology © 2011 Mac Keith Press. |
Affiliation:
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Department of Neurology-Child Neurology, University Hospital and University of Antwerp, Belgium. berten.ceulemans@uza.be |
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From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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