Document Detail


Otolaryngologic manifestations of multiple pterygium syndrome.
MedLine Citation:
PMID:  8770680     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Escobar Syndrome, or Multiple Pterygium Syndrome (MPS), is a rare syndrome with multiple congenital anomalies involving the head and neck area and limbs. Affected individuals have multiple pterygia, camptodactyly and/or syndactyly as the main features of this syndrome. Patients with MPS have a characteristic facies, including ptosis, antimongoloid slant of the palpebral fissures, hypertelorism, micrognathia, neck pterygia, and a sad flat, emotionless look to the face. We present a case of MPS recently treated at our institution for the purpose of further describing the clinical features of this syndrome, emphasizing the otolaryngologic manifestations. Increased awareness of MPS will facilitate appropriate management of this syndrome.
Authors:
C J MacArthur; S Pereira
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  International journal of pediatric otorhinolaryngology     Volume:  34     ISSN:  0165-5876     ISO Abbreviation:  Int. J. Pediatr. Otorhinolaryngol.     Publication Date:  1996 Jan 
Date Detail:
Created Date:  1996-10-03     Completed Date:  1996-10-03     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  8003603     Medline TA:  Int J Pediatr Otorhinolaryngol     Country:  IRELAND    
Other Details:
Languages:  eng     Pagination:  135-40     Citation Subset:  IM    
Affiliation:
Department of Otolaryngology, University of California, Irvine, Orange 92668, USA.
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / genetics,  physiopathology*
Airway Obstruction / diagnosis,  etiology*,  therapy
Face / abnormalities
Female
Gastrostomy
Hand Deformities, Congenital / physiopathology
Humans
Infant
Neck / abnormalities
Otorhinolaryngologic Diseases / diagnosis,  etiology*,  therapy
Pterygium / congenital*,  genetics
Syndrome
Tracheotomy

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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