| Osteogenesis imperfecta associated with basilar impression and cerebral atrophy: a case report. | |
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MedLine Citation:
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PMID: 2743295 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Osteogenesis imperfecta is a disease of bone formation subdivided into two types, congenita and tarda. It is associated with bony fragility, blue sclerae and abnormality of tooth dentin. Rarely the tarda form is associated with basilar invagination or infolding of the foramen magnum and upper cervical segments into the posterior fossa. This results in hydrocephalus and a spectrum of neurologic dysfunction known as the foramen magnum compression syndrome. Many radiologic methods have been used to evaluate basilar invagination including plain film and CT. We describe a patient with osteogenesis imperfecta tarda examined with CT, with a unique finding of diffuse cerebral atrophy associated with basilar invagination. |
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Authors:
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M L Brooks; C Gall; A M Wang; R Schick; C L Rumbaugh |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Computerized medical imaging and graphics : the official journal of the Computerized Medical Imaging Society Volume: 13 ISSN: 0895-6111 ISO Abbreviation: Comput Med Imaging Graph Publication Date: 1989 Jul-Aug |
Date Detail:
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Created Date: 1989-08-15 Completed Date: 1989-08-15 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 8806104 Medline TA: Comput Med Imaging Graph Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 363-7 Citation Subset: IM |
Affiliation:
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Graduate Hospital Imaging Center, Philadelphia, PA 19146. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adult Atrophy Brain Diseases / pathology* Female Humans Osteogenesis Imperfecta / complications* Platybasia / complications* |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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