| Orofacial findings in the Klippel-Trénaunay syndrome. | |
| | |
MedLine Citation:
|
PMID: 11484474 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
|
The Klippel-Trénaunay syndrome is a triad of congenital anomalies characterised by haemangiomas, varicosities, and unilateral bony and soft tissue hypertrophy. Hypertrophy usually affects one distal limb, but trunk or face may be affected. Cutaneous haemangiomas (nevus flammeus) of varying extent and irregular contour are often present in the hypertrophic regions. Varicosities may also be part of the vascular lesions of the syndrome. Orofacial manifestations include facial asymmetry, jaw enlargement, and malocclusions as well as premature tooth eruption. Two cases of the Klippel-Trénaunay syndrome are presented here. Both of these show the typical hemifacial hypertrophy and premature eruption of teeth on the affected side. In the first case only the left mandibular region was affected. In contrast, in the second there was hypertrophy of the whole left side of the body including upper and lower jaws. This boy also suffers from congenital ideokinetic retardation, while the first was otherwise normal. Both cases differ from previously reported cases of the Klippel-Trénaunay syndrome in lacking any prominent facial nevus flammeus. In the first case there was also malformation of the crown of the first permanent molar on the affected side that has not been described previously. |
| | |
Authors:
|
V Mueller-Lessmann; A Behrendt; W E Wetzel; K Petersen; D Anders |
Related Documents
:
|
10327144 - Prenatal sonographic appearances of klippel-trenaunay-weber syndrome. 9820414 - Extensive small bowel varices as a cause of severe anemia in klippel-trenaunay-weber sy... 10325854 - Epidural analgesia in an obstetric patient with klippel-trenaunay syndrome. 16775654 - Between wallenberg syndrome and hemimedullary lesion: cestan-chenais and babinski-nageo... 1564744 - Olfactory neuroblastoma associated with kallman's syndrome. 20236154 - Solitary caecal ulcer syndrome: our experience with this benign condition. |
Publication Detail:
|
Type: Case Reports; Journal Article |
Journal Detail:
|
Title: International journal of paediatric dentistry / the British Paedodontic Society [and] the International Association of Dentistry for Children Volume: 11 ISSN: 0960-7439 ISO Abbreviation: Int J Paediatr Dent Publication Date: 2001 May |
Date Detail:
|
Created Date: 2001-08-03 Completed Date: 2001-09-20 Revised Date: 2004-11-17 |
Medline Journal Info:
|
Nlm Unique ID: 9107511 Medline TA: Int J Paediatr Dent Country: England |
Other Details:
|
Languages: eng Pagination: 225-9 Citation Subset: D |
Affiliation:
|
Department of Paediatric Dentistry, Dental Clinic, Justus-Liebig University, Schlangenzahl 14, D-35392 Giessen, Germany. |
Export Citation:
|
APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
|
Child Face / abnormalities* Facial Asymmetry / pathology Female Hamartoma / pathology Hemangioma / pathology Humans Klippel-Trenaunay-Weber Syndrome / pathology* Male Mandible / abnormalities Maxilla / abnormalities Mental Retardation / pathology Molar / abnormalities Mouth Abnormalities / pathology* Skin Diseases / pathology Skin Neoplasms / pathology Tooth Crown / abnormalities Tooth Eruption Varicose Veins / pathology |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
Previous Document: Intranasal tooth as a complication of cleft lip and alveolus in a four year old child: case report a...
Next Document: Histologic classification of penile carcinoma and its relation to outcome in 61 patients with primar...