Document Detail


Orofacial aspects in Noonan syndrome: 2 case report.
MedLine Citation:
PMID:  18505655     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Noonan syndrome (NS) is an autosomal dominant disorder characterized by dysmorphic facial features in association with short stature and heart disease. A webbed neck, chest deformities, mental retardation, and bleeding disorders are also frequently associated with this pathology. NS is relatively common, with an estimated incidence of 1 per 1,000 to 1 per 2,500 live births. Many cases have been reported in the dental literature, yet only a few of them describe some details of the oral features. The aim of this paper is to describe 2 cases of Noonan syndrome, emphasizing oral and facial aspects and particularities of the dental treatment in subjects affected by this genetic disease.
Authors:
Adriana de Oliveira Lira Ortega; Renata de Oliveira Guaré; Nilce Samecima Kawaji; Ana Lídia Ciamponi
Related Documents :
25412125 - Improved data reporting in rqes: from volumes 49, 59, to 84.
19887225 - Cauda equina syndrome: a literature review of its definition and clinical presentation.
19894475 - Anti-phospholipid syndrome in nigeria: report of five cases.
123255 - Werner's syndrome: autopsy report of one case, with a review of pathologic findings rep...
11992485 - Phenotypic spectrum of interstitial 7p duplication in mosaic and non-mosaic forms.
18700425 - Coblation-assisted lingual tonsillectomy for dysphagia secondary to tongue base hypertr...
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of dentistry for children (Chicago, Ill.)     Volume:  75     ISSN:  1935-5068     ISO Abbreviation:  J Dent Child (Chic)     Publication Date:    2008 Jan-Apr
Date Detail:
Created Date:  2008-05-28     Completed Date:  2008-07-28     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101180951     Medline TA:  J Dent Child (Chic)     Country:  United States    
Other Details:
Languages:  eng     Pagination:  85-90     Citation Subset:  D; IM    
Affiliation:
Federal University of São Paulo, Brazil. aliraort@uol.com.br
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Adolescent
Cephalometry
Deglutition Disorders / etiology
Dental Care for Chronically Ill*
Dental Caries / complications
Dental Plaque / complications
Facies
Gingivitis / complications
Humans
Male
Malocclusion, Angle Class II / etiology*
Noonan Syndrome / complications*
Prognathism / etiology*
Retrognathism / etiology*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Radicular cyst in a deciduous tooth: a case report and literature review.
Next Document:  A report of 2 cases of green pigmentation in the primary dentition associated with cholestasis cause...