Document Detail

Orofacial aspects in Noonan syndrome: 2 case report.
MedLine Citation:
PMID:  18505655     Owner:  NLM     Status:  MEDLINE    
Noonan syndrome (NS) is an autosomal dominant disorder characterized by dysmorphic facial features in association with short stature and heart disease. A webbed neck, chest deformities, mental retardation, and bleeding disorders are also frequently associated with this pathology. NS is relatively common, with an estimated incidence of 1 per 1,000 to 1 per 2,500 live births. Many cases have been reported in the dental literature, yet only a few of them describe some details of the oral features. The aim of this paper is to describe 2 cases of Noonan syndrome, emphasizing oral and facial aspects and particularities of the dental treatment in subjects affected by this genetic disease.
Adriana de Oliveira Lira Ortega; Renata de Oliveira Guaré; Nilce Samecima Kawaji; Ana Lídia Ciamponi
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of dentistry for children (Chicago, Ill.)     Volume:  75     ISSN:  1935-5068     ISO Abbreviation:  J Dent Child (Chic)     Publication Date:    2008 Jan-Apr
Date Detail:
Created Date:  2008-05-28     Completed Date:  2008-07-28     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101180951     Medline TA:  J Dent Child (Chic)     Country:  United States    
Other Details:
Languages:  eng     Pagination:  85-90     Citation Subset:  D; IM    
Federal University of São Paulo, Brazil.
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MeSH Terms
Deglutition Disorders / etiology
Dental Care for Chronically Ill*
Dental Caries / complications
Dental Plaque / complications
Gingivitis / complications
Malocclusion, Angle Class II / etiology*
Noonan Syndrome / complications*
Prognathism / etiology*
Retrognathism / etiology*

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