| Oral findings in ankyloblepharon-ectodermal dysplasia-cleft lip/palate (AEC) syndrome. | |
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MedLine Citation:
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PMID: 19681142 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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This article outlines the dental conditions and treatment findings of individuals ranging in age from 4 months to 30 years of age diagnosed with ankyloblepharon-ectodermal dysplasia-cleft lip/palate (AEC) syndrome. The average number of permanent teeth present is 4.75 with a range of 0-12 teeth. The most frequently present permanent teeth are first molars, canines and maxillary incisors. The dentition of AEC-affected individuals in our study is similar to reports in other ectodermal dysplasia syndromes. The dental treatment findings, including those necessitated by the cleft palate defect seen in the syndrome, are also similar to age appropriate treatment seen in other cases of ectodermal dysplasia syndromes. Only 22% of subjects had prosthetic replacement of missing teeth. History indicated that issues related to treatment of the palatal cleft and lack of recognition of the oral defects as a part of the underlying medical problem were factors in receiving comprehensive tooth replacement care. |
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Authors:
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Frank Farrington; Leonard Lausten |
Publication Detail:
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Type: Journal Article; Research Support, Non-U.S. Gov't |
Journal Detail:
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Title: American journal of medical genetics. Part A Volume: 149A ISSN: 1552-4833 ISO Abbreviation: Am. J. Med. Genet. A Publication Date: 2009 Sep |
Date Detail:
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Created Date: 2009-08-26 Completed Date: 2010-01-05 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 101235741 Medline TA: Am J Med Genet A Country: United States |
Other Details:
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Languages: eng Pagination: 1907-9 Citation Subset: IM |
Copyright Information:
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(c) 2009 Wiley-Liss, Inc. |
Affiliation:
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Virginia Commonwealth University School of Dentistry, Pediatric Dentistry, 521 North 11th Street, Richmond, VA 23298, USA. fhfarrin@vcu.edu |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Abnormalities, Multiple
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diagnosis,
genetics,
pathology Adolescent Adult Anodontia / diagnosis, genetics, pathology* Child Child, Preschool Cleft Lip / diagnosis, genetics, pathology* Cleft Palate / diagnosis, genetics, pathology* Dentition* Ectodermal Dysplasia / diagnosis, genetics, pathology* Eyelids / abnormalities* Female Humans Infant Male Syndrome Young Adult |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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