| Optic neuropathy in McCune-Albright syndrome: an indication for aggressive treatment. | |
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MedLine Citation:
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PMID: 9641748 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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McCune-Albright syndrome consists of the triad polyostotic fibrous dysplasia, café-au-lait spots and autonomous hyperfunction of one or more endocrine systems. The most frequent neurological complication of craniofacial fibrous dysplasia is visual loss. We describe a 17-y-old boy with McCune-Albright syndrome and acute loss of vision in the left eye caused by encroachment of the left optic nerve by fibrous dysplastic lesions. Neurosurgical intervention improved left eye vision. Aggressive intervention is indicated in cases of acute visual loss in patients with craniofacial fibrous dysplasia. This is supported by a review of other reported cases. |
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Authors:
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G Bocca; J de Vries; J R Cruysberg; G H Boers; L A Monnens |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Acta paediatrica (Oslo, Norway : 1992) Volume: 87 ISSN: 0803-5253 ISO Abbreviation: Acta Paediatr. Publication Date: 1998 May |
Date Detail:
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Created Date: 1998-08-04 Completed Date: 1998-08-04 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 9205968 Medline TA: Acta Paediatr Country: NORWAY |
Other Details:
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Languages: eng Pagination: 599-600 Citation Subset: IM |
Affiliation:
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Department of Paediatrics, University Hospital Nijmegen St Radboud, The Netherlands. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adolescent Facial Bones* Fibrous Dysplasia, Polyostotic / complications, surgery* Humans Male Optic Nerve Diseases / complications, surgery* Skull* |
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