| Opercular syndrome without opercular lesions: Foix-Chavany-Marie syndrome in progressive supranuclear motor system degeneration. | |
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MedLine Citation:
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PMID: 2144237 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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A patient is described with slowly progressive supranuclear motor system degeneration (primary lateral sclerosis) characterized by pure bulbar spasticity for six years until a spastic tetraparesis developed. Clinically and electrophysiologically there was and still is no evidence of lower motor neuron involvement. Recently the patient presented with a syndrome of complete inability to move face and tongue voluntarily with preservation of the ability to move them "automatically", e.g. within gestures: automatic-voluntary motor dissociation. Loss of voluntary innervation of the facio-pharyngo-glossomasticatory muscles with preservation of involuntary innervation are the features of the Foix-Chavany-Marie syndrome, which to date has most often been described in association with bilateral vascular lesions of the opercula or their cortigofugal projections. |
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Authors:
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M Weller; M Poremba; J Dichgans |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: European archives of psychiatry and neurological sciences Volume: 239 ISSN: 0175-758X ISO Abbreviation: Eur Arch Psychiatry Neurol Sci Publication Date: 1990 |
Date Detail:
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Created Date: 1990-10-09 Completed Date: 1990-10-09 Revised Date: 2009-11-19 |
Medline Journal Info:
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Nlm Unique ID: 8411522 Medline TA: Eur Arch Psychiatry Neurol Sci Country: GERMANY, WEST |
Other Details:
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Languages: eng Pagination: 370-2 Citation Subset: IM |
Affiliation:
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Department of Neurology, University Clinic, Tübingen, Federal Republic of Germany. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Amyotrophic Lateral Sclerosis
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diagnosis* Cerebral Cortex / pathology* Diagnosis, Differential Dysarthria / diagnosis Hereditary Sensory and Motor Neuropathy / diagnosis* Humans Magnetic Resonance Imaging* Male Middle Aged Muscles / innervation Nerve Degeneration / physiology Neurologic Examination Paralysis / diagnosis* Spastic Paraplegia, Hereditary / diagnosis* Syndrome |
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