| Olmsted syndrome--congenital palmoplantar and periorificial keratoderma. | |
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MedLine Citation:
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PMID: 6232300 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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We are reporting the third case of the Olmsted syndrome, an entity that has received little attention in the medical literature. The syndrome consists of congenital diffuse, sharply marginated keratoderma of the palms and soles, onychodystrophy , constrictions of digits, and periorificial keratoses. Our patient, in addition, had congenital universal alopecia, absence of a premolar tooth, leukokeratosis of oral tissue, and hyperlaxity of the joints. The differential diagnosis includes hidrotic ectodermal dysplasia of the Clouston type, pachyonychia congenita, acrodermatitis enteropathica, keratoma hereditarium mutilans of Vohwinkel , mal de Meleda , and other forms of palmoplantar keratodermas . This patient had originally been reported as having acrodermatitis enteropathica, a condition with which the Olmsted syndrome can easily be confused. |
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Authors:
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Y Poulin; H O Perry; S A Muller |
Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Journal of the American Academy of Dermatology Volume: 10 ISSN: 0190-9622 ISO Abbreviation: J. Am. Acad. Dermatol. Publication Date: 1984 Apr |
Date Detail:
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Created Date: 1984-06-20 Completed Date: 1984-06-20 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 7907132 Medline TA: J Am Acad Dermatol Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 600-10 Citation Subset: IM |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adult Alopecia / congenital Biopsy Diagnosis, Differential Humans Joint Instability / congenital Keratoderma, Palmoplantar / congenital*, diagnosis, pathology Male Pedigree Skin / pathology Syndrome |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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