Document Detail


Oculodentodigital dysplasia syndrome. Report of four cases.
MedLine Citation:
PMID:  197779     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Four cases of oculodentodigital dysplasia are reported. Three cases are from the same family, father and two daughers. These three cases have the characteristics typical of this disorder: narrow nose, hypoplastic alae nasi, microphthalmia, defects of the teeth, syndactylyl of the IV and V fingers, and skeletal anomalies. The fourth case differs from the earlier reported cases; he has all the typical findings of oculodentodigital dysplasia but in addition he shows features not previously reported, namely exceptionally poor vision, mental retardation, monilethrix and pili annuli changes of the hair.
Authors:
C J Thodén; S Ryöppy; P Kuitunen
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Acta paediatrica Scandinavica     Volume:  66     ISSN:  0001-656X     ISO Abbreviation:  Acta Paediatr Scand     Publication Date:  1977 Sep 
Date Detail:
Created Date:  1977-10-28     Completed Date:  1977-10-28     Revised Date:  2009-11-11    
Medline Journal Info:
Nlm Unique ID:  0000211     Medline TA:  Acta Paediatr Scand     Country:  SWEDEN    
Other Details:
Languages:  eng     Pagination:  635-8     Citation Subset:  IM    
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple
Adult
Amelogenesis Imperfecta
Child, Preschool
Dental Enamel Hypoplasia
Eye Abnormalities*
Female
Humans
Male
Mental Retardation
Syndactyly*
Syndrome
Tooth Abnormalities*
Vision Disorders / congenital

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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