Document Detail


Oculo-facio-cardio-dental syndrome in a mother and daughter.
MedLine Citation:
PMID:  16829040     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Oculo-facio-cardio-dental (OFCD) syndrome is a rare X-linked dominant syndrome characterized by canine teeth with extremely large roots (radiculomegaly), congenital cataract, dysmorphic facial features and congenital heart disease. A case of mother-daughter vertical transmission of OFCD is reported. Dental findings were important in confirming the diagnosis in the mother.
Authors:
E McGovern; M Al-Mudaffer; C McMahon; D Brosnahan; P Fleming; W Reardon
Publication Detail:
Type:  Case Reports; Journal Article     Date:  2006-07-10
Journal Detail:
Title:  International journal of oral and maxillofacial surgery     Volume:  35     ISSN:  0901-5027     ISO Abbreviation:  Int J Oral Maxillofac Surg     Publication Date:  2006 Nov 
Date Detail:
Created Date:  2006-10-30     Completed Date:  2007-02-08     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8605826     Medline TA:  Int J Oral Maxillofac Surg     Country:  Denmark    
Other Details:
Languages:  eng     Pagination:  1060-2     Citation Subset:  D; IM    
Affiliation:
Dental Department, Our Lady's Hospital for Sick Children, Crumlin, Dublin 12, Ireland. Eleanor.mcgovern@dental.tcd.ie
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / diagnosis*
Adult
Eye Abnormalities / diagnosis
Female
Genetic Diseases, X-Linked / diagnosis*
Heart Defects, Congenital / diagnosis
Humans
Infant, Newborn
Rare Diseases / diagnosis
Syndrome
Tooth Abnormalities / diagnosis*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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