Document Detail


Ocular and generalized myasthenia gravis induced by human acetylcholine receptor γ subunit immunization.
MedLine Citation:
PMID:  22246876     Owner:  NLM     Status:  In-Data-Review    
Abstract/OtherAbstract:
Introduction: HLA-DQ8 transgenic mice develop ocular myasthenia gravis (oMG), which then progresses to generalized MG (gMG) when immunized with the human acetylcholine receptor (H-AChR) α subunit. Because the fetal AChR γ subunit is expressed in adult extraocular muscles, we anticipated that γ subunit immunization would generate an immune response to mouse AChR and induce MG in mice. Results: H-AChR γ subunit immunization in HLA-DQ8 mice induced an autoimmune response to mouse AChR and led to the destruction of AChR in the neuromuscular junction (NMJ) by anti-AChR antibody and complement activation, and it triggered upregulation of AChR gene transcription. Conclusion: Our findings indicate that oMG may be induced by immunity to the AChR γ subunit. Muscle Nerve, 2012.
Authors:
Xiaorong Wu; Erdem Tuzun; Jing Li; Tianlin Xiao; Shamsher S Saini; Huibin Qi; Windy Allman; Premkumar Christadoss
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Muscle & nerve     Volume:  45     ISSN:  1097-4598     ISO Abbreviation:  Muscle Nerve     Publication Date:  2012 Feb 
Date Detail:
Created Date:  2012-01-16     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  7803146     Medline TA:  Muscle Nerve     Country:  United States    
Other Details:
Languages:  eng     Pagination:  209-16     Citation Subset:  IM    
Copyright Information:
Copyright © 2011 Wiley Periodicals, Inc.
Affiliation:
Department of Ophthalmology, Second Xiangya Hospital, Central South University, Changsha, China.
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