Document Detail


Ocular findings in Brazilian identical twins with Cohen syndrome: case report.
MedLine Citation:
PMID:  20098905     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A case of identical male twins with Cohen syndrome who present multiple ophthalmic findings is reported. The patients were identical 16 year-old twin boys who showed down slanting eyelids, mild ptosis, high-grade myopia, small cortical lens opacities, posterior subcapsular cataracts, myotic and corectopic pupils with poor dilation due to focal iris atrophy and retinochoroidal dystrophy. Ophthalmologists must be aware of the ocular and systemic findings of Cohen syndrome in the evaluation of young patients with mental retardation and visual impairment.
Authors:
Priscila Hae Hyun Rim; Eug?nio Santana de Figueir?do; Fabio Endo Hirata; Carlos Eduardo Steiner; Antonia Paula Marques-de-Faria
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Arquivos brasileiros de oftalmologia     Volume:  72     ISSN:  1678-2925     ISO Abbreviation:  Arq Bras Oftalmol     Publication Date:    2009 Nov-Dec
Date Detail:
Created Date:  2010-01-25     Completed Date:  2010-05-07     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  0400645     Medline TA:  Arq Bras Oftalmol     Country:  Brazil    
Other Details:
Languages:  eng     Pagination:  815-8     Citation Subset:  IM    
Affiliation:
Departament of Ophthalmo/Otorhinolaringology, Universidade Estadual de Campinas, Campinas, SP, Brazil. priscilarim@uol.com.br
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / diagnosis*
Adolescent
Brazil
Diseases in Twins*
Eye Diseases / diagnosis*
Humans
Male
Mental Retardation / diagnosis*
Syndrome
Twins, Monozygotic*

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