| Occipito-atlanto-axial fusion in Morquio-Brailsford syndrome. A ten-year experience. | |
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MedLine Citation:
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PMID: 8666648 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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In 17 patients (eleven males, six females) with Morquio-Brailsford syndrome (mucopolysaccharidosis IV) we have used onlay femoral and tibial autografts placed posteriorly and secured to the laminae of C1 and C2 to obtain satisfactory occipito-C1/C2 posterior fusion. They were immobilised postoperatively in a halo-plaster body jacket for four months. The age at operation varied between three and 28 years. Those with myelopathic symptoms of recent onset made some recovery, but severely myelopathic patients showed little or no recovery. We advise prophylactic occipitocervical fusion in these patients since the cartilaginous dens is not strong enough to ensure atlanto-axial mechanical stability. |
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Authors:
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A O Ransford; H A Crockard; J M Stevens; S Modaghegh |
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Publication Detail:
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Type: Journal Article |
Journal Detail:
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Title: The Journal of bone and joint surgery. British volume Volume: 78 ISSN: 0301-620X ISO Abbreviation: J Bone Joint Surg Br Publication Date: 1996 Mar |
Date Detail:
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Created Date: 1996-08-08 Completed Date: 1996-08-08 Revised Date: 2010-11-10 |
Medline Journal Info:
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Nlm Unique ID: 0375355 Medline TA: J Bone Joint Surg Br Country: ENGLAND |
Other Details:
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Languages: eng Pagination: 307-13 Citation Subset: AIM; IM |
Affiliation:
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Royal National Orthopaedic Hospital NHS Trust, Stanmore, Middlesex, UK. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adolescent Adult Atlanto-Axial Joint / radiography, surgery* Atlanto-Occipital Joint / radiography, surgery* Bone Transplantation / methods Child Child, Preschool Female Humans Male Mucopolysaccharidosis IV / surgery* Spinal Fusion / methods* Transplantation, Autologous |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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