Document Detail


Obstetric anesthesia considerations in Kearns-Sayre syndrome: a case report.
MedLine Citation:
PMID:  25368789     Owner:  NLM     Status:  PubMed-not-MEDLINE    
Abstract/OtherAbstract:
Kearns-Sayre syndrome (KSS) is a rare mitochondrial myopathy that usually develops before 20 years of age. It demonstrates multisystemic involvement with a triad of cardinal features: progressive ophthalmoplegia, pigmentary retinopathy, and cardiac conduction abnormalities. In addition, patients might have cerebellar ataxia, a high content of protein in the cerebrospinal fluid, proximal myopathy, multiple endocrinopathies, and renal tubular acidosis. We herein report the successful obstetric analgesic and anesthetic management of a 28-year-old parturient patient with KSS who required labor analgesia and proceeded to deliver by cesarean section. We extrapolate that regional analgesia/anesthesia might be beneficial for reducing the metabolic demands associated with the stress and pain of labor in patients with KSS. Efficient postoperative analgesia should be provided to decrease oxygen requirements.
Authors:
Ali S Faris; Qutaiba A Tawfic; Leo Jeyaraj
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Publication Detail:
Type:  Journal Article     Date:  2014-10-27
Journal Detail:
Title:  Korean journal of anesthesiology     Volume:  67     ISSN:  2005-6419     ISO Abbreviation:  Korean J Anesthesiol     Publication Date:  2014 Oct 
Date Detail:
Created Date:  2014-11-04     Completed Date:  2014-11-04     Revised Date:  2014-11-06    
Medline Journal Info:
Nlm Unique ID:  101502451     Medline TA:  Korean J Anesthesiol     Country:  Korea (South)    
Other Details:
Languages:  eng     Pagination:  283-6     Citation Subset:  -    
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