| Obstetric anesthesia considerations in Kearns-Sayre syndrome: a case report. | |
MedLine Citation:
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PMID: 25368789 Owner: NLM Status: PubMed-not-MEDLINE |
Abstract/OtherAbstract:
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Kearns-Sayre syndrome (KSS) is a rare mitochondrial myopathy that usually develops before 20 years of age. It demonstrates multisystemic involvement with a triad of cardinal features: progressive ophthalmoplegia, pigmentary retinopathy, and cardiac conduction abnormalities. In addition, patients might have cerebellar ataxia, a high content of protein in the cerebrospinal fluid, proximal myopathy, multiple endocrinopathies, and renal tubular acidosis. We herein report the successful obstetric analgesic and anesthetic management of a 28-year-old parturient patient with KSS who required labor analgesia and proceeded to deliver by cesarean section. We extrapolate that regional analgesia/anesthesia might be beneficial for reducing the metabolic demands associated with the stress and pain of labor in patients with KSS. Efficient postoperative analgesia should be provided to decrease oxygen requirements. |
Authors:
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Ali S Faris; Qutaiba A Tawfic; Leo Jeyaraj |
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Publication Detail:
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Type: Journal Article Date: 2014-10-27 |
Journal Detail:
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Title: Korean journal of anesthesiology Volume: 67 ISSN: 2005-6419 ISO Abbreviation: Korean J Anesthesiol Publication Date: 2014 Oct |
Date Detail:
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Created Date: 2014-11-04 Completed Date: 2014-11-04 Revised Date: 2014-11-06 |
Medline Journal Info:
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Nlm Unique ID: 101502451 Medline TA: Korean J Anesthesiol Country: Korea (South) |
Other Details:
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Languages: eng Pagination: 283-6 Citation Subset: - |
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