Document Detail


Noonan syndrome: prenatal diagnosis in a woman carrying a PTPN11 gene mutation.
MedLine Citation:
PMID:  20064076     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
OBJECTIVE: To describe the case of a pregnant woman and her fetus with Noonan syndrome (NS) whom were diagnosed through ultrasonography 3D and molecular analysis of the PTPN11 gene. STUDY DESIGN: Case report. RESULTS: We detected in a pregnant woman and her child the G<A transition at position 236 in exon 3 of the PTPN11 gene causative of NS. Antenatal diagnosis was possible through ultrasonography in the 24th week of gestation. CONCLUSIONS: Ultrasonography 3D is useful in the antenatal diagnosis of major congenital anomalies. Molecular studies should also be included to confirm the specific diagnosis.
Authors:
Norma Celia González-Huerta; Juan Manuel Valdés-Miranda; Adrián Pérez-Cabrera; Guillermo Pacheco-Cuellar; Luz Maria González-Huerta; Sergio Alberto Cuevas-Covarrubias
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Publication Detail:
Type:  Case Reports; Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  The journal of maternal-fetal & neonatal medicine : the official journal of the European Association of Perinatal Medicine, the Federation of Asia and Oceania Perinatal Societies, the International Society of Perinatal Obstetricians     Volume:  23     ISSN:  1476-4954     ISO Abbreviation:  J. Matern. Fetal. Neonatal. Med.     Publication Date:  2010 Jul 
Date Detail:
Created Date:  2010-06-14     Completed Date:  2010-09-29     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101136916     Medline TA:  J Matern Fetal Neonatal Med     Country:  England    
Other Details:
Languages:  eng     Pagination:  688-91     Citation Subset:  IM    
Affiliation:
Servicio de Genética, Instituto Nacional de Rehabilitación, Hospital General de México, Facultadde Medicina, Universidad Nacional Autónoma de México, México DF, México.
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MeSH Terms
Descriptor/Qualifier:
Adult
Base Sequence
DNA Mutational Analysis
Female
Genetic Testing
Heterozygote
Humans
Imaging, Three-Dimensional
Mutation* / physiology
Noonan Syndrome / diagnosis*,  genetics
Pregnancy
Protein Tyrosine Phosphatase, Non-Receptor Type 11 / genetics*
Ultrasonography, Prenatal* / methods
Chemical
Reg. No./Substance:
EC 3.1.3.48/PTPN11 protein, human; EC 3.1.3.48/Protein Tyrosine Phosphatase, Non-Receptor Type 11

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