Document Detail


A new syndrome associated with absence of lower lid lacrimal punctum, ptosis, elevation deficiency of both eyes and mild facial dysmorphism.
MedLine Citation:
PMID:  19941420     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A considerable volume of literature has been published on the association of lacrimal outflow dysgenesis with developmental anomalies or systemic syndromes. We report three affected individuals in a consanguineous family those are associated with bilateral ptosis, upper ocular movement limitation, and absence of the lacrimal punctum. T our knowledge, this is the first article reporting the association of bilateral ptosis, facial dysmorphism, upper ocular movement limitation, and absence of the lacrimal punctum in a hereditary form. As a sole example, these findings may be accepted as a new syndrome with autosomal recessive pattern because of consanguinity.
Authors:
Sefik Guran; Deniz Torun; Fatih Mehmet Mutlu; Yusuf Uysal; Mehmet Sahin Ugurel; Muhterem Bahce
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Ophthalmic genetics     Volume:  30     ISSN:  1744-5094     ISO Abbreviation:  Ophthalmic Genet.     Publication Date:  2009 Sep 
Date Detail:
Created Date:  2009-11-27     Completed Date:  2010-02-16     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9436057     Medline TA:  Ophthalmic Genet     Country:  England    
Other Details:
Languages:  eng     Pagination:  146-51     Citation Subset:  IM    
Affiliation:
Department of Medical Biology, Medical Faculty, G?lhane Military Medical Academy, Ankara, Turkey. sefguran@yahoo.com
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MeSH Terms
Descriptor/Qualifier:
Adult
Blepharoptosis / genetics*
Consanguinity
Craniofacial Abnormalities / genetics*
Eyelids / abnormalities*
Female
Humans
Lacrimal Apparatus / abnormalities*
Male
Ocular Motility Disorders / genetics*
Pedigree
Syndrome
Young Adult

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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