Document Detail


Neutrophils activate plasmacytoid dendritic cells by releasing self-DNA-peptide complexes in systemic lupus erythematosus.
MedLine Citation:
PMID:  21389263     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Systemic lupus erythematosus (SLE) is a severe and incurable autoimmune disease characterized by chronic activation of plasmacytoid dendritic cells (pDCs) and production of autoantibodies against nuclear self-antigens by hyperreactive B cells. Neutrophils are also implicated in disease pathogenesis; however, the mechanisms involved are unknown. Here, we identified in the sera of SLE patients immunogenic complexes composed of neutrophil-derived antimicrobial peptides and self-DNA. These complexes were produced by activated neutrophils in the form of web-like structures known as neutrophil extracellular traps (NETs) and efficiently triggered innate pDC activation via Toll-like receptor 9 (TLR9). SLE patients were found to develop autoantibodies to both the self-DNA and antimicrobial peptides in NETs, indicating that these complexes could also serve as autoantigens to trigger B cell activation. Circulating neutrophils from SLE patients released more NETs than those from healthy donors; this was further stimulated by the antimicrobial autoantibodies, suggesting a mechanism for the chronic release of immunogenic complexes in SLE. Our data establish a link between neutrophils, pDC activation, and autoimmunity in SLE, providing new potential targets for the treatment of this devastating disease.
Authors:
Roberto Lande; Dipyaman Ganguly; Valeria Facchinetti; Loredana Frasca; Curdin Conrad; Josh Gregorio; Stephan Meller; Georgios Chamilos; Rosalie Sebasigari; Valeria Riccieri; Roland Bassett; Hideki Amuro; Shirou Fukuhara; Tomoki Ito; Yong-Jun Liu; Michel Gilliet
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Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  Science translational medicine     Volume:  3     ISSN:  1946-6242     ISO Abbreviation:  Sci Transl Med     Publication Date:  2011 Mar 
Date Detail:
Created Date:  2011-03-10     Completed Date:  2011-07-06     Revised Date:  2011-11-11    
Medline Journal Info:
Nlm Unique ID:  101505086     Medline TA:  Sci Transl Med     Country:  United States    
Other Details:
Languages:  eng     Pagination:  73ra19     Citation Subset:  IM    
Affiliation:
Department of Immunology, University of Texas M. D. Anderson Cancer Center, Houston, TX 77030, USA.
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MeSH Terms
Descriptor/Qualifier:
Antibodies, Antinuclear / blood
Antigen-Antibody Complex / blood
Autoantigens / blood
B-Lymphocytes / immunology
Case-Control Studies
Cathelicidins / immunology
DNA / blood,  immunology
Dendritic Cells / immunology*
Humans
Lupus Erythematosus, Systemic / immunology*
Lymphocyte Activation
Neutrophils / immunology*
Peptides / blood,  immunology
Toll-Like Receptor 9 / metabolism
Chemical
Reg. No./Substance:
0/Antibodies, Antinuclear; 0/Antigen-Antibody Complex; 0/Autoantigens; 0/Cathelicidins; 0/Peptides; 0/TLR9 protein, human; 0/Toll-Like Receptor 9; 0/antimicrobial peptide LL-37; 9007-49-2/DNA
Comments/Corrections
Comment In:
EMBO Mol Med. 2011 Oct;3(10):578-80   [PMID:  21905225 ]
Nat Rev Rheumatol. 2011 May;7(5):252   [PMID:  21468147 ]
Sci Transl Med. 2011 Mar 9;3(73):73ps9   [PMID:  21389262 ]

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