| Neurofibromatosis-1 and Ampullary Gangliocytic Paraganglioma Causing Biliary and Pancreatic Obstruction. | |
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MedLine Citation:
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PMID: 12754392 Owner: NLM Status: Publisher |
Abstract/OtherAbstract:
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Gangliocytic paragangliomas (GPs) are exceedingly rare tumors that arise in close proximity of the papillaof Vater. Nevertheless, jaundice is an uncommon presenting symptom, reported in only 3 of 125 casesdescribed in the literature to date, with gastrointestinal bleeding being more common.Association between GPs and neurofibromatosis 1 (NF-1), described in two patients, may be more thancasual, being the frequency in normal population 1:3000.We report an additional case of this association, presenting for the first time with simultaneous obstructionof the common biliary duct, and of the main pancreatic duct. Previous cases of GPs with jaundice and/orNF-1 are reviewed, and updating of the histogenesis presented. |
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Authors:
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Laura Castoldi; Paolo De Rai; Aldo Marini; Stefano Ferrero; Valeria De Luca; Giorgio Tiberio |
Publication Detail:
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Type: JOURNAL ARTICLE |
Journal Detail:
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Title: International journal of gastrointestinal cancer Volume: 29 ISSN: 1537-3649 ISO Abbreviation: Int J Gastrointest Cancer Publication Date: 2001 |
Date Detail:
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Created Date: 2003-May-19 Completed Date: - Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 101135379 Medline TA: Int J Gastrointest Cancer Country: - |
Other Details:
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Languages: ENG Pagination: 93-98 Citation Subset: - |
Affiliation:
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Istituto di Chirurgia d'urgenza, Ospedale Maggiore,Via F. Sforza 35, 20122 Milano, Italia. |
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From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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