Document Detail

Neurofibromatosis-1 and Ampullary Gangliocytic Paraganglioma Causing Biliary and Pancreatic Obstruction.
MedLine Citation:
PMID:  12754392     Owner:  NLM     Status:  Publisher    
Gangliocytic paragangliomas (GPs) are exceedingly rare tumors that arise in close proximity of the papillaof Vater. Nevertheless, jaundice is an uncommon presenting symptom, reported in only 3 of 125 casesdescribed in the literature to date, with gastrointestinal bleeding being more common.Association between GPs and neurofibromatosis 1 (NF-1), described in two patients, may be more thancasual, being the frequency in normal population 1:3000.We report an additional case of this association, presenting for the first time with simultaneous obstructionof the common biliary duct, and of the main pancreatic duct. Previous cases of GPs with jaundice and/orNF-1 are reviewed, and updating of the histogenesis presented.
Laura Castoldi; Paolo De Rai; Aldo Marini; Stefano Ferrero; Valeria De Luca; Giorgio Tiberio
Publication Detail:
Journal Detail:
Title:  International journal of gastrointestinal cancer     Volume:  29     ISSN:  1537-3649     ISO Abbreviation:  Int J Gastrointest Cancer     Publication Date:  2001  
Date Detail:
Created Date:  2003-May-19     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101135379     Medline TA:  Int J Gastrointest Cancer     Country:  -    
Other Details:
Languages:  ENG     Pagination:  93-98     Citation Subset:  -    
Istituto di Chirurgia d'urgenza, Ospedale Maggiore,Via F. Sforza 35, 20122 Milano, Italia.
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