Document Detail


Neurocutaneous melanomatosis with a rapidly deteriorating course.
MedLine Citation:
PMID:  12591651     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Neurocutaneous melanosis is a rare congenital syndrome characterized by large or multiple congenital melanocytic nevi and benign or malignant pigment cell tumors of the leptomeninges. The prognosis is extremely poor for symptomatic patients, even in the absence of malignant melanoma. We present serial MR imaging findings in the brain and spine of a child with congenital giant hairy nevi who developed progressive leptomeningeal melanomatosis and whose neurologic condition rapidly deteriorated.
Authors:
Winnie C W Chu; Vincent Lee; Yu-leung Chan; Matthew M K Shing; Ki-wai Chik; Chi-kong Li; Kwok-chiu Ma
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  AJNR. American journal of neuroradiology     Volume:  24     ISSN:  0195-6108     ISO Abbreviation:  AJNR Am J Neuroradiol     Publication Date:  2003 Feb 
Date Detail:
Created Date:  2003-02-19     Completed Date:  2003-04-25     Revised Date:  2008-02-14    
Medline Journal Info:
Nlm Unique ID:  8003708     Medline TA:  AJNR Am J Neuroradiol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  287-90     Citation Subset:  IM    
Affiliation:
Department of Diagnostic Radiology and Organ Imaging, The Chinese University of Hong Kong, Prince of Wales Hospital, 30-32 Ngan Shing Street, Shatin, Hong Kong, China.
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MeSH Terms
Descriptor/Qualifier:
Child, Preschool
Disease Progression
Fatal Outcome
Female
Humans
Magnetic Resonance Imaging*
Melanoma / congenital*,  diagnosis,  pathology
Melanosis / congenital*,  diagnosis,  pathology
Meningeal Neoplasms / congenital*,  diagnosis,  pathology
Meninges / pathology
Meningitis / diagnosis,  pathology
Neurocutaneous Syndromes / congenital*,  diagnosis,  pathology
Nevus, Pigmented / congenital*,  diagnosis,  pathology
Spinal Cord / pathology
Status Epilepticus / diagnosis,  pathology
Temporal Lobe / pathology

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