Document Detail


Neuro-ophthalmologic manifestations of Maffucci's syndrome and Ollier's disease.
MedLine Citation:
PMID:  10098552     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Patients with Ollier's disease (multiple skeletal enchondromas) and Maffucci's syndrome (multiple enchondromas associated with subcutaneous hemangiomas) may develop skull base chondrosarcomas or low-grade astrocytomas as a delayed consequence of these disorders. We report three patients with Ollier's disease and Maffucci's syndrome who had diplopia as the initial manifestation of intracranial tumors. Since patients with Maffucci's syndrome and Ollier's disease are at risk for the delayed development of brain and systemic neoplasms, neuroophthalmologists must be aware of the need for long-term surveillance in patients affected by these conditions.
Authors:
L J Balcer; S L Galetta; W T Cornblath; G T Liu
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of neuro-ophthalmology : the official journal of the North American Neuro-Ophthalmology Society     Volume:  19     ISSN:  1070-8022     ISO Abbreviation:  J Neuroophthalmol     Publication Date:  1999 Mar 
Date Detail:
Created Date:  1999-04-23     Completed Date:  1999-04-23     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  9431308     Medline TA:  J Neuroophthalmol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  62-6     Citation Subset:  IM    
Affiliation:
Department of Neurology, Hospital of the University of Pennsylvania, Scheie Eye Institute, University of Pennsylvania School of Medicine, Philadelphia, USA.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Abducens Nerve / pathology
Adolescent
Adult
Astrocytoma / diagnosis*
Brain / pathology
Brain Neoplasms / diagnosis*
Chondrosarcoma / diagnosis*
Cranial Nerve Diseases / diagnosis
Diplopia / diagnosis*
Enchondromatosis / diagnosis*
Facial Nerve / pathology
Facial Nerve Diseases / diagnosis
Female
Humans
Magnetic Resonance Imaging
Male
Paralysis / diagnosis
Skull / pathology
Skull Base Neoplasms / diagnosis*
Trigeminal Nerve / pathology

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Endoscopic sinus surgery in the management of mucormycosis.
Next Document:  Optic atrophy and chronic acquired polyneuropathy.