Document Detail


Neural mechanisms in Williams syndrome: a unique window to genetic influences on cognition and behaviour.
MedLine Citation:
PMID:  16760918     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Williams syndrome, a rare disorder caused by hemizygous microdeletion of about 28 genes on chromosome 7q11.23, has long intrigued neuroscientists with its unique combination of striking behavioural abnormalities, such as hypersociability, and characteristic neurocognitive profile. Williams syndrome, therefore, raises fundamental questions about the neural mechanisms of social behaviour, the modularity of mind and brain development, and provides a privileged setting to understand genetic influences on complex brain functions in a 'bottom-up' way. We review recent advances in uncovering the functional and structural neural substrates of Williams syndrome that provide an emerging understanding of how these are related to dissociable genetic contributions characterized both in special participant populations and animal models.
Authors:
Andreas Meyer-Lindenberg; Carolyn B Mervis; Karen Faith Berman
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Publication Detail:
Type:  Journal Article; Research Support, N.I.H., Extramural; Research Support, N.I.H., Intramural; Review    
Journal Detail:
Title:  Nature reviews. Neuroscience     Volume:  7     ISSN:  1471-003X     ISO Abbreviation:  Nat. Rev. Neurosci.     Publication Date:  2006 May 
Date Detail:
Created Date:  2006-06-08     Completed Date:  2006-07-13     Revised Date:  2012-05-28    
Medline Journal Info:
Nlm Unique ID:  100962781     Medline TA:  Nat Rev Neurosci     Country:  England    
Other Details:
Languages:  eng     Pagination:  380-93     Citation Subset:  IM    
Affiliation:
Unit for Systems Neuroscience in Psychiatry, National Institute of Mental Health, NIH, DHHS, 9000 Rockville Pike, Bethesda, Maryland 20892-1365, USA.
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MeSH Terms
Descriptor/Qualifier:
Animals
Behavior / physiology*
Brain / blood supply,  pathology,  physiopathology*
Cognition / physiology*
Humans
Image Processing, Computer-Assisted / methods
Magnetic Resonance Imaging / methods
Social Behavior
Williams Syndrome* / genetics,  pathology,  physiopathology
Grant Support
ID/Acronym/Agency:
R01 NS035102/NS/NINDS NIH HHS

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