Document Detail


Neither SP-A nor NH2-terminal domains of SP-A can substitute for SP-D in regulation of alveolar homeostasis.
MedLine Citation:
PMID:  16500946     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Surfactant proteins (SP)-A and -D are members of the collectin family of host defense proteins that share four distinct structural domains: NH(2)-terminal oligomerization, collagenous, neck, and carbohydrate recognition (CRD). To determine the specificity of the functions of these domains, the SFTPC promoter was used to express 1) full-length rat (r) Sftpa; 2) NH(2)-rSftpa/d, consisting of NH(2)-terminal and collagenous domains of SP-A with neck domain and CRD of SP-D; and 3) rSftpd/a, consisting of NH(2)-terminal and collagenous domains of SP-D with neck domain and CRD of SP-A, in Sftpd(-/-) mice. Increased expression of SP-A in Sftpd(-/-) mice did not correct the increased pulmonary saturated phosphatidylcholine levels, emphysema, or foamy alveolar macrophage and lymphocyte infiltrations characteristic of Sftpd(-/-) mice, indicating that the decreased SP-A level noted in Sftpd(-/-) mice does not account for the observed pulmonary abnormalities. The chimeric protein NH(2)-rSftpa/d was expressed and detected in the airways of transgenic mice, migrating as an SP-A-like oligomer that associated with large aggregate surfactant in a manner similar to that of SP-A rather than SP-D. NH(2)-rSftpa/d did not correct emphysema, foamy macrophage and lymphocyte infiltration, or the increased lipid accumulations characteristic of Sftpd(-/-) mice. Thus oligomerization and surfactant lipid association of SP-D requires its NH(2)-terminal and collagenous domains, which are needed for SP-D-dependent regulation of surfactant homeostasis in vivo. Attempts to express rSftpd/a fusion protein in vivo were unsuccessful. Mmp9(-/-)/Sftpd(-/-) and Mmp12(-/-)/Sftpd(-/-) mice developed air space enlargement similar to Sftpd(-/-) mice, supporting the concept that the increased expression of each metalloproteinase seen in Sftpd(-/-) lungs is not the major cause of emphysema.
Authors:
Liqian Zhang; Machiko Ikegami; Thomas R Korfhagen; Francis X McCormack; Mitsuhiro Yoshida; Robert M Senior; J Michael Shipley; Steven D Shapiro; Jeffrey A Whitsett
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Publication Detail:
Type:  Journal Article; Research Support, N.I.H., Extramural     Date:  2006-02-24
Journal Detail:
Title:  American journal of physiology. Lung cellular and molecular physiology     Volume:  291     ISSN:  1040-0605     ISO Abbreviation:  Am. J. Physiol. Lung Cell Mol. Physiol.     Publication Date:  2006 Aug 
Date Detail:
Created Date:  2006-07-07     Completed Date:  2006-09-26     Revised Date:  2007-11-14    
Medline Journal Info:
Nlm Unique ID:  100901229     Medline TA:  Am J Physiol Lung Cell Mol Physiol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  L181-90     Citation Subset:  IM    
Affiliation:
Division of Pulmonary Biology, Cincinnati Children's Hospital Medical Center, OH 45229, USA.
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MeSH Terms
Descriptor/Qualifier:
Animals
Bronchoalveolar Lavage Fluid / chemistry,  cytology
Homeostasis*
Lipids / chemistry
Mice
Mice, Knockout
Mice, Transgenic
Protein Structure, Tertiary
Pulmonary Alveoli / cytology,  metabolism*,  pathology
Pulmonary Surfactant-Associated Protein A / genetics,  metabolism*
Pulmonary Surfactant-Associated Protein D / genetics,  metabolism*
Rats
Recombinant Fusion Proteins / genetics,  metabolism
Grant Support
ID/Acronym/Agency:
HL-47328/HL/NHLBI NIH HHS; HL-56387/HL/NHLBI NIH HHS; HL-58795/HL/NHLBI NIH HHS; HL-63329/HL/NHLBI NIH HHS; HL-68861/HL/NHLBI NIH HHS
Chemical
Reg. No./Substance:
0/Lipids; 0/Pulmonary Surfactant-Associated Protein A; 0/Pulmonary Surfactant-Associated Protein D; 0/Recombinant Fusion Proteins

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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