Document Detail

Myotonic dystrophy initially presenting as tachycardiomyopathy successful catheter ablation of atrial flutter.
MedLine Citation:
PMID:  20871860     Owner:  NLM     Status:  In-Data-Review    
Myotonic dystrophy is a genetic muscular disease that is frequently associated with cardiac arrhythmias. Bradyarrhythmias, such as sinus bradycardia and atrioventricular block, are more common than tachyarrhythmias. Rarely, previously undiagnosed patients with myotonic dystrophy initially present with a tachyarrhythmia. We describe the case of a 14-year-old boy, who was admitted to the hospital with clinical signs and symptoms of decompensated heart failure and severely reduced left ventricular function. Electrocardiography showed common-type atrial flutter with 2 : 1 conduction resulting in a heart rate of 160 bpm. Initiation of medical therapy for heart failure as well as electrical cardioversion led to a marked clinical improvement. Catheter ablation of atrial flutter was performed to prevent future cardiac decompensations and to prevent development of tachymyopathy. Left ventricular function normalized during followup. Genetic analysis confirmed the clinical suspicion of myotonic dystrophy as known in other family members in this case.
S Asbach; K J Gutleben; P Dahlem; J Brachmann; G Nölker
Publication Detail:
Type:  Journal Article     Date:  2010-08-24
Journal Detail:
Title:  Cardiology research and practice     Volume:  2010     ISSN:  2090-0597     ISO Abbreviation:  Cardiol Res Pract     Publication Date:  2010  
Date Detail:
Created Date:  2010-09-27     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  101516542     Medline TA:  Cardiol Res Pract     Country:  Egypt    
Other Details:
Languages:  eng     Pagination:  -     Citation Subset:  -    
II. Medizinische Klinik, Klinikum Coburg, 96450 Coburg, Germany.
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