Document Detail


Myelodysplastic syndrome with trisomy 8 associated with Behçet syndrome: an immunologic link to a karyotypic abnormality.
MedLine Citation:
PMID:  17066465     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Myelodysplastic syndrome (MDS) in children is often associated with chromosomal anomalies and trisomy 8 is a characteristic karyotypic feature in up to 20% of the cases. Behçet disease is a rare multisystem inflammatory disorder characterized by recurrent mouth and genital ulcers. MDS with trisomy 8 has been observed in adult patients with Behçet syndrome with some cases developing prior to the clinical manifestations of the latter. We present a female with a similar association and explain the importance of identifying the coexisting conditions. The immunological abnormalities, which may be observed in MDS and their possible mechanisms, are also discussed.
Authors:
Jecko V Thachil; Rahuman Salim; Anne Field; Robert Moots; Paula Bolton-Maggs
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  Pediatric blood & cancer     Volume:  50     ISSN:  1545-5017     ISO Abbreviation:  Pediatr Blood Cancer     Publication Date:  2008 Mar 
Date Detail:
Created Date:  2008-01-15     Completed Date:  2008-02-12     Revised Date:  2009-01-12    
Medline Journal Info:
Nlm Unique ID:  101186624     Medline TA:  Pediatr Blood Cancer     Country:  United States    
Other Details:
Languages:  eng     Pagination:  649-51     Citation Subset:  IM    
Copyright Information:
(c) 2007 Wiley-Liss, Inc.
Affiliation:
Department of Haematology, Royal Liverpool University Hospital, Liverpool, United Kingdom. jeckothachil@yahoo.co.uk
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Anemia, Refractory / etiology*,  genetics,  immunology
Behcet Syndrome / diagnosis,  drug therapy,  genetics*,  immunology
Chromosomes, Human, Pair 8*
Female
Humans
Immunologic Deficiency Syndromes / etiology
Immunosuppressive Agents / therapeutic use
Karyotyping
Oral Ulcer / drug therapy,  etiology
Tacrolimus / therapeutic use
Thalidomide / therapeutic use
Trisomy*
Chemical
Reg. No./Substance:
0/Immunosuppressive Agents; 109581-93-3/Tacrolimus; 50-35-1/Thalidomide

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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