Document Detail

Muscle computed tomography in adult-onset acid maltase deficiency.
MedLine Citation:
PMID:  9486870     Owner:  NLM     Status:  MEDLINE    
Nine patients with adult-onset acid maltase deficiency (Pompe's disease) were examined clinically and with computed tomography (CT). The CT scan showed early and severe involvement of the muscles of trunk and thighs, with selective sparing of the tensor fasciae latae, short head of biceps femoris, gracilis, and sartorius muscles. Shoulder and leg muscles were less affected. The disease spread over the years from trunk to extremities. Muscle strength and CT findings were positively correlated.
A E de Jager; T M van der Vliet; T C van der Ree; B J Oosterink; M C Loonen
Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  Muscle & nerve     Volume:  21     ISSN:  0148-639X     ISO Abbreviation:  Muscle Nerve     Publication Date:  1998 Mar 
Date Detail:
Created Date:  1998-03-13     Completed Date:  1998-03-13     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  7803146     Medline TA:  Muscle Nerve     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  398-400     Citation Subset:  IM    
Department of Neurology, University Hospital Groningen, The Netherlands.
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MeSH Terms
Age of Onset
Disease Progression
Glycogen Storage Disease Type II / physiopathology*,  radiography
Middle Aged
Muscle, Skeletal / physiopathology,  radiography*
Tomography, X-Ray Computed
alpha-Glucosidases / deficiency*
Reg. No./Substance:

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