Document Detail


Multiple neoplasms following craniospinal irradiation for medulloblastoma in a patient with nevoid basal cell carcinoma syndrome. Case report.
MedLine Citation:
PMID:  9010431     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A 28-year-old man presented to the authors' hospital with multiple intracranial tumors. At 2 years of age, he had undergone resection of a medulloblastoma and received adjunctive craniospinal irradiation. Subsequently, he was diagnosed with nevoid basal cell carcinoma syndrome, Gorlin's syndrome. Since his first presentation, he has required surgery for multiple basal cell carcinomas, an osteochondroma of the rib, two meningiomas, a trigeminal schwannoma, and a pleomorphic liposarcoma, all of which arose within the radiation field. Despite this impressive list of benign and malignant neoplasms, the patient is relatively well and leads a normal life. The authors examine the relationships between Gorlin's syndrome and radiation therapy and the subsequent development of tumors.
Authors:
S O'Malley; D Weitman; M Olding; L Sekhar
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of neurosurgery     Volume:  86     ISSN:  0022-3085     ISO Abbreviation:  J. Neurosurg.     Publication Date:  1997 Feb 
Date Detail:
Created Date:  1997-02-13     Completed Date:  1997-02-13     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  0253357     Medline TA:  J Neurosurg     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  286-8     Citation Subset:  AIM; IM    
Affiliation:
Department of Neurosurgery, George Washington University School of Medicine and Health Sciences, Washington, D.C., USA.
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MeSH Terms
Descriptor/Qualifier:
Adult
Basal Cell Nevus Syndrome / diagnosis,  etiology*,  surgery
Bone Neoplasms / surgery
Brain Neoplasms / etiology*,  surgery
Cerebellar Neoplasms / radiotherapy*,  surgery
Humans
Liposarcoma / surgery
Male
Medulloblastoma / radiotherapy*,  surgery
Neoplasms, Radiation-Induced* / surgery
Ribs

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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