| Multiple intrapulmonary arteriovenous fistulas in childhood. | |
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MedLine Citation:
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PMID: 10982718 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Pulmonary arteriovenous fistulas (AVFs) are a rare but recognized cause of cyanosis in childhood. Lesions may be acquired as in hepatopulmonary syndrome or they may be congenital, particularly in association with certain multisystem disorders. Large fistulas are more common than multiple small connections. Two cases. both boys, presenting in the first decade of life are described. "Bubble" echocardiography was the most telling investigation and strongly suggested the presence of AVFs in both cases. Each patient then underwent cardiac catheterization, which demonstrated normal pulmonary artery pressure and diffuse pulmonary telangiectasis. Both patients were treated effectively with nifedipine and continue with this mode of therapy. |
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Authors:
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A Sands; E Dalzell; B Craig; M Shields |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Pediatric cardiology Volume: 21 ISSN: 0172-0643 ISO Abbreviation: Pediatr Cardiol Publication Date: 2000 Sep-Oct |
Date Detail:
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Created Date: 2000-12-15 Completed Date: 2001-01-04 Revised Date: 2008-02-20 |
Medline Journal Info:
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Nlm Unique ID: 8003849 Medline TA: Pediatr Cardiol Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 493-6 Citation Subset: IM |
Affiliation:
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Department of Paediatric Cardiology, Royal Belfast Hospital for Sick Children, United Kingdom. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Abnormalities, Multiple* Arteriovenous Fistula* / complications, diagnosis, drug therapy Child Cyanosis / etiology* Dyskeratosis Congenita Humans Male Nifedipine / therapeutic use Pulmonary Artery / abnormalities* Pulmonary Veins / abnormalities* Syndrome Telangiectasis / radiography Vasodilator Agents / therapeutic use |
| Chemical | |
Reg. No./Substance:
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0/Vasodilator Agents; 21829-25-4/Nifedipine |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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