Document Detail


Multiple intrapulmonary arteriovenous fistulas in childhood.
MedLine Citation:
PMID:  10982718     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Pulmonary arteriovenous fistulas (AVFs) are a rare but recognized cause of cyanosis in childhood. Lesions may be acquired as in hepatopulmonary syndrome or they may be congenital, particularly in association with certain multisystem disorders. Large fistulas are more common than multiple small connections. Two cases. both boys, presenting in the first decade of life are described. "Bubble" echocardiography was the most telling investigation and strongly suggested the presence of AVFs in both cases. Each patient then underwent cardiac catheterization, which demonstrated normal pulmonary artery pressure and diffuse pulmonary telangiectasis. Both patients were treated effectively with nifedipine and continue with this mode of therapy.
Authors:
A Sands; E Dalzell; B Craig; M Shields
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Pediatric cardiology     Volume:  21     ISSN:  0172-0643     ISO Abbreviation:  Pediatr Cardiol     Publication Date:    2000 Sep-Oct
Date Detail:
Created Date:  2000-12-15     Completed Date:  2001-01-04     Revised Date:  2008-02-20    
Medline Journal Info:
Nlm Unique ID:  8003849     Medline TA:  Pediatr Cardiol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  493-6     Citation Subset:  IM    
Affiliation:
Department of Paediatric Cardiology, Royal Belfast Hospital for Sick Children, United Kingdom.
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple*
Arteriovenous Fistula* / complications,  diagnosis,  drug therapy
Child
Cyanosis / etiology*
Dyskeratosis Congenita
Humans
Male
Nifedipine / therapeutic use
Pulmonary Artery / abnormalities*
Pulmonary Veins / abnormalities*
Syndrome
Telangiectasis / radiography
Vasodilator Agents / therapeutic use
Chemical
Reg. No./Substance:
0/Vasodilator Agents; 21829-25-4/Nifedipine

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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