Document Detail

Modified Fontan procedure for severe Ebstein's malformation with predominant tricuspid stenosis.
MedLine Citation:
PMID:  1510520     Owner:  NLM     Status:  MEDLINE    
Two children, aged 7 and 6 years, had severe Ebstein's malformation of the tricuspid valve and underwent operation because of progressive cyanosis (saturation, 70%). Preoperative angiography demonstrated linear attachment of the distal edges of the displaced anterosuperior and mural leaflets, leaving only a "keyhole" communication between the atrialized and functional portions of the right ventricle. Operation was directed toward completely excising these dysplastic leaflets, which were obstructing the flow of blood. The continuity between the functional right ventricle and pulmonary trunk was left intact. In addition, an atriopulmonary truncal connection was established. Postoperatively, both children were in functional class I with arterial saturation of 95%. Angiography and Doppler echocardiography demonstrated that there was a dominant phase of systolic flow of blood up the pulmonary trunk from the right ventricle, and also diastolic filling of the pulmonary arteries through the atriopulmonary truncal connection. The filling patterns did not change over time for the follow-up period of 4 and 1.5 years, respectively. This modified Fontan procedure appears to be an effective surgical alternative for some patients with severe Ebstein's malformation and predominant tricuspid stenosis.
M P Leung; J Lee; R N Lo; C K Mok
Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  The Annals of thoracic surgery     Volume:  54     ISSN:  0003-4975     ISO Abbreviation:  Ann. Thorac. Surg.     Publication Date:  1992 Sep 
Date Detail:
Created Date:  1992-09-23     Completed Date:  1992-09-23     Revised Date:  2007-11-15    
Medline Journal Info:
Nlm Unique ID:  15030100R     Medline TA:  Ann Thorac Surg     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  523-6; discussion 526-7     Citation Subset:  AIM; IM    
Department of Paediatrics, Grantham Hospital, University of Hong Kong.
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MeSH Terms
Ebstein Anomaly / complications,  physiopathology,  radiography,  surgery*
Heart / radiography
Tricuspid Valve Stenosis / complications*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

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