| Migraine-like attacks in child with Sturge-Weber syndrome without facial nevus. | |
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MedLine Citation:
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PMID: 15664776 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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The Sturge-Weber syndrome was recently subdivided into type I (facial and leptomeningeal angioma, possible glaucoma), type II (facial angioma, without evident endocranial involvement), and type III (exclusive leptomeningeal angioma). Thus far in the literature only 24 cases of Sturge-Weber syndrome type III have been reported. This study presents a case of a 2-year 9-month-old child with normal psychomotor development and skin free (no angiomas), who presented repeated episodes of severe headache, vertiginous symptoms, vomiting, and drowsiness, separated by complete recovery. The cranial computed tomography and magnetic resonance imaging with gadolinium revealed left occipital leptomeningeal angiomatosis with calcifications, suggesting a diagnosis of Sturge-Weber syndrome type III. Considering the normal psychomotor development, the improved electroencephalographic reports between the episodes, and the absence of hypoperfusion areas on single-photon emission computed tomography at 30 months of follow-up, the symptomatology appears an expression of migraine-like symptoms resulting from vasomotor disturbances within and around the angioma, more than an expression of partial seizures arising through an epileptic focus in the ischemic region around the vascular malformation. |
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Authors:
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Grazia Taddeucci; Alice Bonuccelli; Paola Polacco |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Pediatric neurology Volume: 32 ISSN: 0887-8994 ISO Abbreviation: Pediatr. Neurol. Publication Date: 2005 Feb |
Date Detail:
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Created Date: 2005-01-24 Completed Date: 2005-04-28 Revised Date: 2006-05-23 |
Medline Journal Info:
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Nlm Unique ID: 8508183 Medline TA: Pediatr Neurol Country: United States |
Other Details:
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Languages: eng Pagination: 131-3 Citation Subset: IM |
Affiliation:
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Department of Pediatrics, Section of Pediatric Neurology, University of Studies of Pisa, Via Fermi 9, 56126 Pisa, Italy. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Brain
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pathology,
physiopathology Child, Preschool Humans Male Migraine Disorders / etiology*, pathology, physiopathology Sturge-Weber Syndrome / complications*, pathology, physiopathology |
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